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Pathophys and Cause

Cause:Any vasculitis (Nejm 1997;337:1512) including: giant cell, Takayasu's, polyarteritis, Wegener's, paraneoplastic, inflammatory bowel disease, and immune complex types (anaphylactoid Henoch-Schönlein purpura, cryoglobininemia, SLE, RA, Sjögren's, Goodpastures, Behcet's, scleroderma, and drug- or viral-induced, a continuum from urticaria to erythema multiforme (Urticaria/Erythema Multiforme)

Signs and Symptoms

Si:Bilaterally symmetric, palpable (r/o DIC), hematuria- and guaiac-pos stools, hemorrhagic bullae