Arrhythmogenic Right Ventricular Cardiomyopathy

Avoid competitive sports

Asymptomatic

Symptomatic

Close follow-up

End

β-adrenergic blocker

ICD

Consider amiodarone

Adjunctive therapies to !!DownArrow!!ventricular arrhythmias:

β-adrenergic blockers
Amiodarone
Sotalol
Catheter ablation

Symptomatic PVCs, NSVT

Unexplained syncope

Aborted SCD, sustained VT/VF

^* Risk factors:

Familial ARVC at high risk of SCD
Malignant family history of SCD
LV dysfunction or involvement
Frequent NSVT
Severe RV systolic dysfunction
Late Gd enhancement on cardiac MRI
Marked QRS prolongation
Inducible sustained VT at EP study

Risk factors^*

Yes

No