Major Categories of Noninfectious Vasculitis - Flowchart
Major Categories of Noninfectious Vasculitis - Flowchart Vasculitis, Systemic Vasculitis, Systemic
«Flowchart»

Vasculitis

Vasculitis

Vasculitis

Vasculitis

Small-vessel vasculitis

Small-vessel vasculitis

Small-vessel vasculitis Small-vessel vasculitis

Medium-vessel vasculitis


Polyarteritis nodosa
Kawasaki disease

Medium-vessel vasculitis

Medium-vessel vasculitis


Polyarteritis nodosa
Kawasaki disease


Polyarteritis nodosa
Kawasaki disease Medium-vessel vasculitis

Large-vessel vasculitis


Giant cell arteritis
Takayasu arteritis

Large-vessel vasculitis

Large-vessel vasculitis


Giant cell arteritis
Takayasu arteritis


Giant cell arteritis
Takayasu arteritis Large-vessel vasculitis

End

End

End

EGPA, Eosinophilic granulomatous polyangiitis; GPA, granulomatous polyangiitis; HSP, Henoch-Schönlein purpura.

EGPA, Eosinophilic granulomatous polyangiitis; GPA, granulomatous polyangiitis; HSP, Henoch-Schönlein purpura.

EGPA, Eosinophilic granulomatous polyangiitis; GPA, granulomatous polyangiitis; HSP, Henoch-Schönlein purpura.

EGPA GPA HSP

Circulating antineutrophil cytoplasmic antibodies (ANCA) associated


Microscopic polyangiitis (MPA)
GPA (Wegener)
EGPA (Churg-Strauss)
Drug-induced ANCA-associated vasculitis

Circulating antineutrophil cytoplasmic antibodies (ANCA) associated

Circulating antineutrophil cytoplasmic antibodies (ANCA) associated


Microscopic polyangiitis (MPA)
GPA (Wegener)
EGPA (Churg-Strauss)
Drug-induced ANCA-associated vasculitis


Microscopic polyangiitis (MPA)
GPA (Wegener)
EGPA (Churg-Strauss)
Drug-induced ANCA-associated vasculitis Circulating antineutrophil

Immune-complex associated


Cryoglobulinemic vasculitis
IgA vasculitis (HSP)
Anti-GBM (glomerular basement membrane) disease
Infection-induced immune complex vasculitis (e.g., hepatitis B and C)
Serum sickness vasculitis
Lupus vasculitis
Rheumatoid vasculitis
Hypocomplementemic urticarial vasculitis
Behçet disease
Drug-induced immune-complex vasculitis

Immune-complex associated

Immune-complex associated


Cryoglobulinemic vasculitis
IgA vasculitis (HSP)
Anti-GBM (glomerular basement membrane) disease
Infection-induced immune complex vasculitis (e.g., hepatitis B and C)
Serum sickness vasculitis
Lupus vasculitis
Rheumatoid vasculitis
Hypocomplementemic urticarial vasculitis
Behçet disease
Drug-induced immune-complex vasculitis


Cryoglobulinemic vasculitis
IgA vasculitis (HSP)
Anti-GBM (glomerular basement membrane) disease
Infection-induced immune complex vasculitis (e.g., hepatitis B and C)
Serum sickness vasculitis
Lupus vasculitis
Rheumatoid vasculitis
Hypocomplementemic urticarial vasculitis
Behçet disease
Drug-induced immune-complex vasculitis Immune-complex

Paraneoplastic


Carcinoma-induced vasculitis
Lymphoproliferative neoplasm-induced vasculitis
Myeloproliferative neoplasm-induced vasculitis

Paraneoplastic

Paraneoplastic


Carcinoma-induced vasculitis
Lymphoproliferative neoplasm-induced vasculitis
Myeloproliferative neoplasm-induced vasculitis


Carcinoma-induced vasculitis
Lymphoproliferative neoplasm-induced vasculitis
Myeloproliferative neoplasm-induced vasculitis Paraneoplastic

Inflammatory bowel disease vasculitis

Inflammatory bowel disease vasculitis

Inflammatory bowel disease vasculitis Inflammatory