Decision-Making Pathway in the Management of Chronic Inflammatory Demyelinating Polyradiculoneuropathy (CIDP) - Flowchart
Decision-Making Pathway in the Management of Chronic Inflammatory Demyelinating Polyradiculoneuropathy (CIDP) - Flowchart Chronic Inflammatory Demyelinating Polyneuropathy Chronic Inflammatory Demyelinating Polyneuropathy
«Flowchart»

TREATMENT OF CIDP

TREATMENT OF CIDP

TREATMENT OF CIDP

Observation

Observation

Observation

PE 2-3/wk × 6 wk and prednisone 60-80 mg/day

PE 2-3/wk × 6 wk and prednisone 60-80 mg/day

PE 2-3/wk × 6 wk and prednisone 60-80 mg/day

Diagnosis confirmed

Diagnosis confirmed

Diagnosis confirmed

Mild deficits

Mild deficits

Mild deficits

Functionally significant deficits

Functionally significant deficits

Functionally significant deficits

Severe disease, nonambulatory

Severe disease, nonambulatory

Severe disease, nonambulatory

End

End

End

Improvement

Improvement

Improvement

Start IVIG stop PE taper prednisone

Start IVIG stop PE taper prednisone

Start IVIG stop PE taper prednisone

NA at 4-6 wk

NA at 4-6 wk

NA at 4-6 wk

NA at 6 wk

NA at 6 wk

NA at 6 wk

NA at 3-6 wk

NA at 3-6 wk

NA at 3-6 wk

IVIG 0.4 g/kg × 5 days
or

IVIG 0.4 g/kg × 5 days
or


IVIG 0.4 g/kg × 5 days

Prednisone 60-80 mg/day
or

Prednisone 60-80 mg/day
or


Prednisone 60-80 mg/day

PE 2-3/wk × 6 wk

PE 2-3/wk × 6 wk

PE 2-3/wk × 6 wk

Improvement

Improvement

Improvement

Monthly NA

Monthly NA

Monthly NA

IVIG 1 g/kg/day every 2-4 wk

IVIG 1 g/kg/day every 2-4 wk

IVIG 1 g/kg/day every 2-4 wk

Improvement

Improvement

Improvement

Taper prednisone, qod schedule

Taper prednisone, qod schedule

Taper prednisone, qod schedule

Improvement

Improvement

Improvement

Taper PE schedule, add prednisone

Taper PE schedule, add prednisone

Taper PE schedule, add prednisone