References
- Mouzaki M, Bronsky J, Gupte G, et al. Nutrition support of children with chronic liver diseases: a joint position paper of the North American Society for Pediatric Gastroenterology, Hepatology, and Nutrition and the European Society for Pediatric Gastroenterology, Hepatology, and Nutrition. J Pediatr Gastroenterol Nutr. 2019;69(4):498-511 PMID: 31436707 doi: 10.1097/MPG.0000000000002443
- Tanpowpong P, Broder-Fingert S, Katz AJ, Camargo CA Jr. Predictors of gluten avoidance and implementation of a gluten-free diet in children and adolescents without confirmed celiac disease. J Pediatr. 2012;161(3):471-475 PMID: 22484356 doi: 10.1016/j.jpeds.2012.02.049
- Utterson EC, Shepherd RW, Sokol RJ, et al; SPLIT Research Group. Biliary atresia: clinical profiles, risk factors, and outcomes of 755 patients listed for liver transplantation. J Pediatr. 2005;147(2):180-185 PMID: 16126046 doi: 10.1016/j.jpeds.2005.04.073
- Sundaram SS, Mack CL, Feldman AG, Sokol RJ. Biliary atresia: indications and timing of liver transplantation and optimization of pretransplantion care. Liver Transpl. 2017;23(1):96-109. doi: 10.1002/lt.24640
- Young S, Kwarta E, Azzam R, Sentongo T. Nutrition assessment and support in children with end-stage liver disease. Nutr Clin Pract. 2013;28(3):317-329 PMID: 23466471 doi: 10.1177/0884533612474043
- Hanai T, Shiraki M, Nishimura K, et al. Sarcopenia impairs prognosis of patients with liver cirrhosis. Nutrition. 2015;31(1):193-199 PMID: 25441595 doi: 10.1016/j.nut.2014.07.005
- Montano-Loza AJ. Muscle wasting: a nutritional criterion to prioritize patients for liver transplantation. Curr Opin Clin Nutr Metab Care. 2014;17(3):219-225 PMID: 24613858 doi: 10.1097/MCO.0000000000000046
- Tessitore M, Sorrentino E, Schiano Di Cola G, Colucci A, Vajro P, Mandato C. Malnutrition in pediatric chronic cholestatic disease: an up-to-date overview. Nutrients.2021;13(8):2785 PMID: 34444944 doi: 10.3390/nu13082785
- Gramlich L, Ireton-Jones C, Miles JM, Morrison M, Pontes-Arruda A. Essential fatty acid requirements and intravenous lipid emulsions. JPEN J Parenter Enteral Nutr. 2019;43(6):697-707 PMID: 30908685 doi: 10.1002/jpen.1537
- Pettei MJ, Daftary S, Levine JJ. Essential fatty acid deficiency associated with the use of a medium-chain-triglyceride infant formula in pediatric hepatobiliary disease. Am J Clin Nutr. 1991;53(5):1217-1221 PMID: 2021130 doi: 10.1093/ajcn/53.5.1217
- Kaufman SS, Scrivner DJ, Murray ND, Vanderhoof JA, Hart MH, Antonson DL. Influence of portagen and pregestimil on essential fatty acid status in infantile liver disease. Pediatrics. 1992;89(1):151-154 PMID: 1728003 doi: 10.1542/peds.89.1.151
- Shneider BL, Magee JC, Bezerra JA, et al; Childhood Liver Disease Research Education Network (ChiLDREN). Efficacy of fat-soluble vitamin supplementation in infants with biliary atresia. Pediatrics. 2012;130(3):e607-e614 PMID: 22891232 doi: 10.1542/peds.2011-1423
- Ross AC. Modern Nutrition in Health and Disease. Wolters Kluwer Health/Lippincott Williams & Wilkins; 2014
- Lippe B, Hensen L, Mendoza G, Finerman M, Welch M. Chronic vitamin A intoxication. A multisystem disease that could reach epidemic proportions. Am J Dis Child. 1981;135(7):634-636 PMID: 7246491 doi: 10.1001/archpedi.1981.02130310040014
- Penniston KL, Tanumihardjo SA. The acute and chronic toxic effects of vitamin A. Am J Clin Nutr. 2006;83(2):191-201 PMID: 16469975 doi: 10.1093/ajcn/83.2.191
- Heubi JE, Hollis BW, Specker B, Tsang RC. Bone disease in chronic childhood cholestasis. I. Vitamin D absorption and metabolism. Hepatology. 1989;9(2): 258-264 PMID: 2783577 doi: 10.1002/hep.1840090216
- Bucuvalas JC, Heubi JE, Specker BL, Gregg DJ, Yergey AL, Vieira NE. Calcium absorption in bone disease associated with chronic cholestasis during childhood. Hepatology. 1990;12(5):1200-1205 PMID: 2227818 doi: 10.1002/hep.1840120520
- Heubi JE, Higgins JV, Argao EA, Sierra RI, Specker BL. The role of magnesium in the pathogenesis of bone disease in childhood cholestatic liver disease: a preliminary report. J Pediatr Gastroenterol Nutr. 1997;25(3):301-306 PMID: 9285381 doi: 10.1097/00005176-199709000-00010
- Argao EA, Balistreri WF, Hollis BW, Ryckman FC, Heubi JE. Effect of orthotopic liver transplantation on bone mineral content and serum vitamin D metabolites in infants and children with chronic cholestasis. Hepatology. 1994;20(3):598-603 PMID: 8076918 doi: 10.1002/hep.1840200308
- Högler W, Baumann U, Kelly D. Endocrine and bone metabolic complications in chronic liver disease and after liver transplantation in children. J Pediatr Gastroenterol Nutr. 2012;54(3):313-321 PMID: 22064631 doi: 10.1097/MPG.0b013e31823e9412
- Sokol RJ, Heubi JE, Iannaccone S, Bove KE, Balistreri WF. Mechanism causing vitamin E deficiency during chronic childhood cholestasis. Gastroenterology. 1983;85(5):1172-1182 PMID: 6618108 doi: 10.1016/S0016-5085(83)80087-0
- Guggenheim MA, Jackson V, Lilly J, Silverman A. Vitamin E deficiency and neurologic disease in children with cholestasis: A prospective study. J Pediatr. 1983;102(4):577-579 PMID: 6834194 doi: 10.1016/S0022-3476(83)80189-9
- Sokol RJ, Guggenheim MA, Iannaccone ST, et al. Improved neurologic function after long-term correction of vitamin E deficiency in children with chronic cholestasis. N Engl J Med. 1985;313(25):1580-1586 PMID: 4069170 doi: 10.1056/NEJM198512193132505
- Sokol RJ, Heubi JE, Iannaccone ST, Bove KE, Balistreri WF. Vitamin E deficiency with normal serum vitamin E concentrations in children with chronic cholestasis. N Engl J Med. 1984;310(19):1209-1212 PMID: 6709026 doi: 10.1056/NEJM198405103101901
- Olson RE. The function and metabolism of vitamin K. Annu Rev Nutr. 1984;4(1):281-337 PMID: 6380538 doi: 10.1146/annurev.nu.04.070184.001433
- Nelsestuen GL, Shah AM, Harvey SB. Vitamin K-dependent proteins. Vitam Horm. 2000;58:355-389 PMID: 10668405 doi: 10.1016/S0083-6729(00)58031-5
- Price PA, Parthemore JG, Deftos LJ. New biochemical marker for bone metabolism. Measurement by radioimmunoassay of bone GLA protein in the plasma of normal subjects and patients with bone disease. J Clin Invest. 1980;66(5):878-883 PMID: 6968755 doi: 10.1172/JCI109954
- Bancroft J, Cohen MB. Intracranial hemorrhage due to vitamin K deficiency in breast-fed infants with cholestasis. J Pediatr Gastroenterol Nutr. 1993;16(1):78-80 PMID: 8433245
- Yanofsky RA, Jackson VG, Lilly JR, Stellin G, Klingensmith WC III, Hathaway WE. The multiple coagulopathies of biliary atresia. Am J Hematol. 1984;16(2): 171-180 PMID: 6695916 doi: 10.1002/ajh.2830160209
- Strople J, Lovell G, Heubi J. Prevalence of subclinical vitamin K deficiency in cholestatic liver disease. J Pediatr Gastroenterol Nutr. 2009;49(1):78-84 PMID: 19502999 doi: 10.1097/MPG.0b013e31819a61ff
- Göksu N, Ozsoylu S. Hepatic and serum levels of zinc, copper, and magnesium in childhood cirrhosis. J Pediatr Gastroenterol Nutr. 1986;5(3):459-462 PMID: 3723267 doi: 10.1097/00005176-198605000-00022
- Hambidge KM, Krebs NF, Lilly JR, Zerbe GO. Plasma and urine zinc in infants and children with extrahepatic biliary atresia. J Pediatr Gastroenterol Nutr. 1987;6(6):872-877 PMID: 3681573
- Narkewicz MR, Krebs N, Karrer F, Orban-Eller K, Sokol RJ. Correction of hypozincemia following liver transplantation in children is associated with reduced urinary zinc loss. Hepatology. 1999;29(3):830-833 PMID: 10051486 doi: 10.1002/hep.510290322
- MacKay M, Mulroy CW, Street J, et al. Assessing copper status in pediatric patients receiving parenteral nutrition. Nutr Clin Pract. 2015;30(1):117-121 PMID: 24934222 doi: 10.1177/0884533614538457
- Bayliss EA, Hambidge KM, Sokol RJ, Stewart B, Lilly JR. Hepatic concentrations of zinc, copper and manganese in infants with extrahepatic biliary atresia. J Trace Elem Med Biol. 1995;9(1):40-43 PMID: 8846156 doi: 10.1016/S0946-672X(11)80007-6
- Vinton NE, Dahlstrom KA, Strobel CT, Ament ME. Macrocytosis and pseudoalbinism: manifestations of selenium deficiency. J Pediatr. 1987;111(5): 711-717 PMID: 3117996 doi: 10.1016/S0022-3476(87)80247-0
- Misra M, Pacaud D, Petryk A, Collett-Solberg PF, Kappy M; Drug and Therapeutics Committee of the Lawson Wilkins Pediatric Endocrine Society. Vitamin D deficiency in children and its management: review of current knowledge and recommendations. Pediatrics. 2008;122(2):398-417 PMID: 18676559 doi: 10.1542/peds.2007-1894
- Gluud LL, Dam G, Les I, et al. Branched-chain amino acids for people with hepatic encephalopathy. Cochrane Database Syst Rev. 2015;(2):CD001939 PMID: 25715177
- Pawłowska J. The importance of nutrition for pediatric liver transplant patients. Clin Exp Hepatol. 2016;2(3):105-108 PMID: 28856271 doi: 10.5114/ceh.2016.61665
- Guidance to Liver Transplant Programs and the National Liver Review Board for. Pediatric MELD/PELD Exception Review. Accessed May 30, 2022. http://optn.transplant.hrsa.gov/media/3yqdbemu/liver_guidance_pediatric_meld_201706.pdf
- Wessel A, Rohr F. Inborn errors of metabolism. In: Manual of Pediatric Nutrition. 5th ed; 2014: 461-483
- Schwimmer JB, Deutsch R, Kahen T, Lavine JE, Stanley C, Behling C. Prevalence of fatty liver in children and adolescents. Pediatrics. 2006;118(4):1388-1393 PMID: 17015527 doi: 10.1542/peds.2006-1212
- Promrat K, Kleiner DE, Niemeier HM, et al. Randomized controlled trial testing the effects of weight loss on nonalcoholic steatohepatitis. Hepatology. 2010;51(1): 121-129 PMID: 19827166 doi: 10.1002/hep.23276
- Vilar-Gomez E, Martinez-Perez Y, Calzadilla-Bertot L, et al. Weight loss through lifestyle modification significantly reduces features of nonalcoholic steatohepatitis. Gastroenterology. 2015;149(2):367-78.e5 PMID: 25865049 doi: 10.1053/j.gastro.2015.04.005
- Nobili V, Alisi A, Newton KP, Schwimmer JB. Comparison of the phenotype and approach to pediatric vs adult patients with nonalcoholic fatty liver disease. Gastroenterology. 2016;150(8):1798-1810 PMID: 27003600 doi: 10.1053/j.gastro.2016.03.009
- Lavine JE, Schwimmer JB, Van Natta ML, et al; Nonalcoholic Steatohepatitis Clinical Research Network. Effect of vitamin E or metformin for treatment of nonalcoholic fatty liver disease in children and adolescents: the TONIC randomized controlled trial. JAMA. 2011;305(16):1659-1668 PMID: 21521847 doi: 10.1001/jama.2011.520
- Carter BA, Taylor OA, Prendergast DR, et al. Stigmasterol, a soy lipid-derived phytosterol, is an antagonist of the bile acid nuclear receptor FXR. Pediatr Res. 2007;62(3):301-306 PMID: 17622954 doi: 10.1203/PDR.0b013e3181256492
- El Kasmi KC, Anderson AL, Devereaux MW, et al. Phytosterols promote liver injury and Kupffer cell activation in parenteral nutrition-associated liver disease. Sci Transl Med. 2013;5(206):206ra137 PMID: 24107776 doi: 10.1126/scitranslmed.3006898
- Lacaille F, Gupte G, Colomb V, et al; ESPGHAN Working Group of Intestinal Failure and Intestinal Transplantation. Intestinal failure-associated liver disease: a position paper of the ESPGHAN Working Group of Intestinal Failure and Intestinal Transplantation. J Pediatr Gastroenterol Nutr. 2015;60(2):272-283 PMID: 25272324 doi: 10.1097/MPG.0000000000000586
- Cohran VC, Prozialeck JD, Cole CR. Redefining short bowel syndrome in the 21st century. Pediatr Res. 2017;81(4):540-549 PMID: 27997531 doi: 10.1038/pr.2016.265
- Sanchez SE, Braun LP, Mercer LD, Sherrill M, Stevens J, Javid PJ. The effect of lipid restriction on the prevention of parenteral nutrition-associated cholestasis in surgical infants. J Pediatr Surg. 2013;48(3):573-578 PMID: 23480915 doi: 10.1016/j.jpedsurg.2012.08.016
- Premkumar MH, Carter BA, Hawthorne KM, King K, Abrams SA. Fish oil-based lipid emulsions in the treatment of parenteral nutrition-associated liver disease: an ongoing positive experience. Adv Nutr. 2014;5(1):65-70 PMID: 24425724 doi: 10.3945/an.113.004671
- Pichler J, Simchowitz V, Macdonald S, Hill S. Comparison of liver function with two new/mixed intravenous lipid emulsions in children with intestinal failure. Eur J Clin Nutr. 2014;68(10):1161-1167 PMID: 24961544 doi: 10.1038/ejcn.2014.118
- Dai YJ, Sun LL, Li MY, et al. Comparison of formulas based on lipid emulsions of olive oil, soybean oil, or several oils for parenteral nutrition: a systematic review and meta-analysis. Adv Nutr. 2016;7(2):279-286 PMID: 26980811 doi: 10.3945/an.114.007427
- Diamond IR, Grant RC, Pencharz PB, et al. Preventing the progression of intestinal failure-associated liver disease in infants using a composite lipid emulsion: a pilot randomized controlled trial of SMOFlipid. JPEN J Parenter Enteral Nutr. 2017;41(5):866-877 PMID: 26838529 doi: 10.1177/0148607115626921
- Roberts EA, Schilsky ML; American Association for Study of Liver Diseases (AASLD). Diagnosis and treatment of Wilson disease: an update. Hepatology. 2008;47(6):2089-2111 PMID: 18506894 doi: 10.1002/hep.22261