A. Primarily Stenoses (Narrowing)
- Radiation Induced Damage
- Homocysteinuria
- Congenital Anomaly: Coarctation of the Aorta
B. Primarily Aneurysm (Dilatation)
- Marfan Syndrome
- Kawasaki Disease
- Syphilis
- Ehlers Danlos Syndrome (mainly Type IV)
- Reiter's Syndrome
- Ankylosing Spondylitis
- Radiation Induced Damage
C. Stenotic and Aneurysmal Lesions
- Atherosclerosis
- Inflammatory Aortitis
- Fibromuscular Dysplasia
D. Inflammatory Aortitis Differential
- Giant Cell Arteritis (GCA) [2]
- Takayasu Arteritis
- Relapsing Polychondritis
- Syphilis
- Cogan Syndrome
References
- Vlahakes GJ, Hanna GJ, Marks EJ. 1998. NEJM. 338(13):897 (Case Record)
- Nuenninghoff DM, Hunder GG, Christianson TJ, et al. 2003. Arthritis Rheum. 48(12):3522
