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A. Primarily Stenoses (Narrowing)

  1. Radiation Induced Damage
  2. Homocysteinuria
  3. Congenital Anomaly: Coarctation of the Aorta

B. Primarily Aneurysm (Dilatation)

  1. Marfan Syndrome
  2. Kawasaki Disease
  3. Syphilis
  4. Ehlers Danlos Syndrome (mainly Type IV)
  5. Reiter's Syndrome
  6. Ankylosing Spondylitis
  7. Radiation Induced Damage

C. Stenotic and Aneurysmal Lesions

  1. Atherosclerosis
  2. Inflammatory Aortitis
  3. Fibromuscular Dysplasia

D. Inflammatory Aortitis Differential

  1. Giant Cell Arteritis (GCA) [2]
  2. Takayasu Arteritis
  3. Relapsing Polychondritis
  4. Syphilis
  5. Cogan Syndrome


References

  1. Vlahakes GJ, Hanna GJ, Marks EJ. 1998. NEJM. 338(13):897 (Case Record)
  2. Nuenninghoff DM, Hunder GG, Christianson TJ, et al. 2003. Arthritis Rheum. 48(12):3522 abstract