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Table 67-1

Clinical Schema of Lymphoid Neoplasms

Chronic Lymphoid Leukemias/Lymphomas

 Chronic lymphocytic leukemia/small lymphocytic lymphoma (99% B cell, 1% T cell)

 Prolymphocytic leukemia (90% B cell, 10% T cell)

 Large granular lymphocyte leukemia (80% NK cell, 20% T cell)

 Hairy cell leukemia (99-100% B cell)

Indolent Lymphoma

 Follicular center cell lymphoma, grades I and II (100% B cell)

 Lymphoplasmacytic lymphoma/Waldenström's macroglobulinemia (100% B cell)

 Marginal zone lymphoma (100% B cell)

  Extranodal (MALT lymphoma)

  Nodal (monocytoid B cell lymphoma)

  Splenic marginal zone lymphoma

 Cutaneous T cell lymphoma (mycosis fungoides) (100% T cell)

Aggressive Lymphoma

 Diffuse large cell lymphoma (85% B cell, 15% T cell) includes immunoblastic

 Follicular center cell lymphoma, grade III (100% B cell)

 Mantle cell lymphoma (100% B cell)

 Primary mediastinal (thymic) large B cell lymphoma (100% B cell)

 Burkitt-like lymphoma (100% B cell)

 Peripheral T cell lymphoma (100% T cell)

 Angioimmunoblastic lymphoma (100% T cell)

 Angiocentric lymphoma (80% T cell, 20% NK cell)

 Intestinal T cell lymphoma (100% T cell)

 Anaplastic large cell lymphoma (70% T cell, 30% null cell)

Acute Lymphoid Leukemias/Lymphomas

 Precursor lymphoblastic leukemia/lymphoma (80% T cell, 20% B cell)

 Burkitt's leukemia/lymphoma (100% B cell)

 Adult T cell leukemia/lymphoma (100% T cell)

Plasma Cell Disorders (100% B cell)

 Monoclonal gammopathy of uncertain significance

 Solitary plasmacytoma

 Extramedullary plasmacytoma

 Multiple myeloma

 Plasma cell leukemia

Hodgkin's Lymphoma (cell of origin mainly B cell)

 Lymphocyte predominant

 Nodular sclerosis

 Mixed cellularity

 Lymphocyte depleted

Abbreviations: MALT, mucosa-associated lymphatic tissue; NK, natural killer.