= relatively benign non-LCH dendritic cell disorder of early childhood

Age:<1 year (majority)

• Skin
  • small yellow-reddish papule / plaque / nodule (early) with usually spontaneous regression within a few years
    Location: head, neck, upper trunk
• Soft tissue
  Location: subcutaneous to deep
  • heterogeneously hypoechoic hypovascular nodule
  • infiltrative nonenhancing mass of intermediate T1 signal
• Bone
  • well-defined medullary lytic lesion with sclerotic margins
• Liver, spleen, lung, bones, lymph nodes, GI tract

Dx: based on typical dermal findings