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Information

Skull and Spine Disorders

= epithelium-lined dural tube extending from skin surface to intracanalicular space + frequently communicating with CNS / its coverings

Cause: focal point of incomplete separation of cutaneous ectoderm from neural ectoderm during neurulation

Age: early childhood to 3rd decade; M÷F = 1÷1

Location: lumbosacral (60%), occipital (25%), thoracic (10%), cervical (2%), sacrococcygeal (1%), ventral (8%)

Course: in a craniad direction from skin level toward cord ascension of cord relative to spinal canal during embryogenesis

Associated with: epidermoid / dermoid tumors in up to 20%

CT myelography (best modality to define intraspinal anatomy):

Cx:

  1. Meningitis (bacterial / chemical)
  2. Subcutaneous / epidural / subdural / subarachnoid / subpial abscess (bacterial ascent)
    • Dermal sinus accounts for up to 3% of spinal cord abscesses!
  3. Compression of neural structures

DDx: pilonidal sinus / simple sacral dimple (no extension to neural structures)