Prevalence: 20 cases reported in literature
Location: spinal cord, intradural-extramedullary compartment, extradural compartment
Age: more common in adults than children; M÷F = 6÷4
Histo: small round blue cells with hyperchromatic nuclei + scanty cytoplasm, frequent mitoses
Spread: throughout CSF space into cranium, lung, bone, lymph node
Prognosis: in >50% death within 2 years