Bone and Soft-Tissue Disorders
= rare benign cartilaginous tumor; initially arising in cortex
Frequency:<1% of all bone tumors
Histo: chondroid + fibrous + myxoid tissue (related to chondroblastoma); may be mistaken for chondrosarcoma
Age: peak 2nd3rd decade (range, 579 years); M÷F = 1÷1
- slowly progressive local pain, swelling, restriction of motion
Location:
- long bones (60%): about knee (50%), proximal tibia (82% of tibial lesions), distal femur (71% of femoral lesions), fibula
- short tubular bones of hand + feet (20%)
- flat bones: pelvis, ribs (classic but uncommon)
Site: metaphyseal (4753%), metadiaphyseal (2043%), metaepiphyseal (26%), diaphyseal (110%), epiphyseal (3%); eccentric
Size: 110 cm in length; 47 cm in width
- expansile ovoid lesion with radiolucent center + oval shape at each end of lesion
- long axis parallel to long axis of host bone
- geographic bone destruction (100%)
- well-defined sclerotic margin (86%)
- expanded shell = bulged + thinned overlying cortex (68%)
- partial cortical erosion (68%)
- scalloped margin (58%)
- septations (57%) may mimic trabeculations
- stippled calcifications within tumor in advanced lesions (7%)
- NO periosteal reaction (unless fractured)
Prognosis: 25% recurrence rate following curettage
Cx: malignant degeneration distinctly unusual
DDx:
- Aneurysmal bone cyst
- Simple bone cyst
- Nonossifying fibroma
- Fibrous dysplasia
- Enchondroma
- Chondroblastoma
- Eosinophilic granuloma
- Fibrous cortical defect
- Giant cell tumor