Skull and Spine Disorders
= CRANIOLACUNIA = LACUNAR SKULL
= mesenchymal dysplasia of calvarial ossification (developmental disturbance)
Age: present at birth
Associated with:
- Meningocele / myelomeningocele / encephalocele
- Spina bifida
- Cleft palate
- Arnold-Chiari II malformation
- normal intracranial pressure
Location: particularly upper parietal area
- honeycombed appearance about 2 cm in diameter (thinning of diploic space)
- premature closure of sutures (turricephaly / scaphocephaly)
Prognosis: spontaneous regression within first 6 months of life
DDx:
- Convolutional impressions = digital markings (visible at 2 years, maximally apparent at 4 years, disappear by 8 years of age)
- Hammered silver appearance of increased intracranial pressure