= combination of posterior spina bifida + meningocele + tethered cord + hydromyelia + cystic dilatation of distal central canal
Cause: disturbed CSF circulation resulting in dilatation of ventriculus terminalis + disruption of dorsal mesenchyme
Associated with: anorectal + genitourinary + vertebral anomalies: anal atresia, cloacal exstrophy, scoliosis, sacral agenesis