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Information

 Bone and Soft-Tissue Disorders

= rare condition increased bone formation within medullary cavity of long bones of lower extremity similar to progressive diaphyseal dysplasia / hereditary multiple diaphyseal sclerosis

Age: adulthood; F >M

Location: uni- / bilateral in 1 long bone of lower extremity; most frequently in tibia

Site: middiaphyseal region

Dx: after exclusion of other causes of osteosclerosis (eg, stress fractures, osteomyelitis, metabolic / endocrine disorders, malignancy)