Both short and long-acting beta-2 agonists may be beneficial both in the short and long term in individuals with cystic fibrosis who have bronchodilator responsiveness or bronchial hyperresponsiveness Inhaled Bronchodilators for Cystic Fibrosis.
There is insufficient evidence to support or oppose the long-term use of oxygen therapy for people with cystic fibrosis. Short-term oxygen therapy may improve oxygenation and exercise capacity.Oxygen Therapy for Cystic Fibrosis.
Non-invasive ventilation as an adjunct to other airway clearance techniques may be useful in improving respiratory function in people with cystic fibrosis, especially those who have difficulty expectorating sputum Non-Invasive Ventilation for Cystic Fibrosis.
Oral calorie supplements appear not to provide any additional benefit in the nutritional management of moderately malnourished children with cystic fibrosis compared to dietary advice and monitoring alone Oral Calorie Supplements for Cystic Fibrosis.