Benign Chronic Familial Pemphigus on the Skin of the Chest

Benign chronic familial pemphigus on the skin of the chest. Benign chronic familial pemphigus (Morbus Hailey-Hailey) on the skin of the chest of a middle-aged woman. The typical clinical picture, histological finding and (for the time being) good response to a moderately potent glucocorticoid ointment support the diagnosis of Morbus Hailey-Hailey and distinguish this case from the most important disease to be taken into account in differential diagnosis, Morbus Darier (dyskeratosis congenita) http://www.orpha.net/en/disease/detail/218.

Picture: Raimo Suhonen