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References
Cystic Fibrosis (CF) - Related Resources
Cochrane reviews
Both short and long-acting
beta-2 agonists
may be beneficial both in the short and long term in individuals with cystic fibrosis
who
have bronchodilator responsiveness
or
bronchial hyperresponsiveness
Inhaled Bronchodilators for Cystic Fibrosis
.
There is insufficient evidence to
support
or oppose the long-term use of
oxygen
therapy for people with cystic fibrosis. Short-term oxygen therapy may improve
oxygenation
and
exercise
capacity.
Oxygen Therapy for Cystic Fibrosis
.
Non-invasive
ventilation
as
an adjunct to
other
airway clearance
techniques
may be useful in improving
respiratory function
in people with cystic fibrosis, especially those who have difficulty expectorating
sputum
Non-Invasive Ventilation for Cystic Fibrosis
.
There is insufficient evidence on the effects of positive expiratory
pressure
(PEP) devices for
chest
physiotherapy
for people with cystic fibrosis
Positive Expiratory Pressure Physiotherapy for Airway Clearance in People with Cystic Fibrosis
.
Omega
-3 supplements may provide some benefits for people with cystic fibrosis with relatively few
adverse effects
Omega-3 Fatty Acids (from Fish Oils) for Cystic Fibrosis
.
Oral
calorie supplements appear not to provide any additional
benefit
in the nutritional
management
of moderately malnourished
children
with cystic fibrosis compared to
dietary advice
and monitoring alone
Oral Calorie Supplements for Cystic Fibrosis
.
Oscillating devices
may not provide any benefit over other methods of physiotherapeutic airway clearance in terms of
lung
function or sputum characteristics in people with cystic fibrosis
Oscillating Devices for Airway Clearance in Cystic Fibrosis
.
Oral
steroids
at
prednisolone
equivalent dose
of 1-2 mg/kg alternate days may slow the
progression
of lung
disease
in cystic fibrosis but cause cataracts and impair
growth
Long-Term Oral Steroids for Cystic Fibrosis
.
Topical
administration
of short-acting
sodium
channel blocker may not improve respiratory condition in people with cystic fibrosis and may even cause a decline in lung function
Sodium Channel Blockers for Cystic Fibrosis
.
Giving anti-staphylococcal
antibiotic prophylaxis
to young children with cystic fibrosis may
lead
to fewer children having isolates of
Staphylococcus aureus
but the clinical importance of this finding is uncertain
Prophylactic Anti-Staphylococcal Antibiotics for Cystic Fibrosis
.
Once and three times daily aminoglycoside antibiotics appear to be equally effective in the
treatment
of pulmonary exacerbations of cystic fibrosis
Once-Daily Dosing of Aminoglycosides for Cystic Fibrosis
.
Drug
therapies that reduce gastric
acidity
seem to improve fat
absorption
and gastro-intestinal
symptoms
such as
abdominal pain
in people with cystic fibrosis, although the evidence is insufficient
Drug Therapies for Reducing Gastric Acidity in People with Cystic Fibrosis
.
Other
Internet
resources
Cystic fibrosis. Orphanet ORPHA586
http://www.orpha.net/consor/cgi-bin/Disease_Search.php?lng=EN&data_id=49&Disease_Disease_Search_diseaseGroup=cystic-fibrosis&Disease_Disease_Search_diseaseType=Pat&Disease(s) concerned=Cystic-fibrosis&title=Cystic-fibrosis&search=Disease_Search_Simple
Literature
Boyle MP.
Adult
cystic fibrosis. JAMA 2007 Oct 17;298(15):1787-93.
[PubMed]
Davies JC, Alton EW, Bush A. Cystic fibrosis. BMJ 2007
Dec
15;335(7632):1255-9.
[PubMed]
Primary/Secondary Keywords
Related resources