Health Promotion and Maintenance
9. An infant in a newborn nursery is identified as having phenylketonuria (PKU). What is the best initial source of nutrients for an infant with this diagnosis?
Health Promotion and Maintenance
9. An infant in a newborn nursery is identified as having phenylketonuria (PKU). What is the best initial source of nutrients for an infant with this diagnosis?
Test-Taking Tip
Note that the stem of the question asks for the best "initial" source of nutrients. Breastfeeding should be started first, and then special formulas may be considered if necessary.
Content Area: Child Health, Gastrointestinal; Integrated Process: Nursing Process, Analysis; Cognitive Level: Application; Client Need/Subneed: Physiological Integrity/Basic Care and Comfort/Nutrition and Oral Hydration
Health Promotion and Maintenance
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Answer 1 is correct because the child with PKU is missing the enzyme needed to digest the amino acid phenylalanine. Maternal breast milk has many beneficial properties and it contains low levels of phenylalanine. Therefore, breast milk should be given until laboratory findings demonstrate the child is not tolerating the breast milk. Answer 2 is incorrect because Pregestimil is an example of a formula containing excessive amounts of phenylalanine and is contraindicated for an infant with PKU. Answer 3 is incorrect. Although Lofenalac is a formula specially made for infants with PKU and contains very low amounts of phenylalanine, maternal breast milk is the best initial source of nutrients. Answer 4 is incorrect because Isomil is an example of a formula containing excessive amounts of phenylalanine and is contraindicated for an infant with PKU.
