Other respiratory diseases principally affecting the interstitium (J80-J84)
J80Acute respiratory distress syndrome
› Acute respiratory distress syndrome in adult or child
› Adult hyaline membrane disease
Excludes 1: respiratory distress syndrome in newborn (perinatal) (P22.0)
J81Pulmonary edema
Use Additional Code: code to identify:
› exposure to environmental tobacco smoke (Z77.22)
› history of tobacco dependence (Z87.891)
› occupational exposure to environmental tobacco smoke (Z57.31)
› tobacco dependence (F17.-)
› tobacco use (Z72.0)
Excludes 1: chemical (acute) pulmonary edema (J68.1)
› hypostatic pneumonia (J18.2)
› passive pneumonia (J18.2)
› pulmonary edema due to external agents (J60-J70)
› pulmonary edema with heart disease NOS (I50.1)
› pulmonary edema with heart failure (I50.1)
J81.0Acute pulmonary edema
› Acute edema of lung
J81.1Chronic pulmonary edema
› Pulmonary congestion (chronic) (passive)
› Pulmonary edema NOS
J82Pulmonary eosinophilia, not elsewhere classified
Excludes 2: pulmonary eosinophilia due to aspergillosis (B44.-)
› pulmonary eosinophilia due to drugs (J70.2-J70.4)
› pulmonary eosinophilia due to specified parasitic infection (B50-B83)
› pulmonary eosinophilia due to systemic connective tissue disorders (M30-M36)
› pulmonary infiltrate NOS (R91.8)
J82.8Pulmonary eosinophilia, not elsewhere classified
J82.81Chronic eosinophilic pneumonia
› Eosinophilic pneumonia, NOS
J82.82Acute eosinophilic pneumonia
J82.83Eosinophilic asthma
Code First: asthma, by type, such as:
› mild intermittent asthma (J45.2-)
› mild persistent asthma (J45.3-)
› moderate persistent asthma (J45.4-)
› severe persistent asthma (J45.5-)
J82.89Other pulmonary eosinophilia, not elsewhere classified
› Allergic pneumonia
› Löffler's pneumonia
› Tropical (pulmonary) eosinophilia NOS
J84Other interstitial pulmonary diseases
Excludes 1: drug-induced interstitial lung disorders (J70.2-J70.4)
› interstitial emphysema (J98.2)
Excludes 2: lung diseases due to external agents (J60-J70)
J84.0Alveolar and parieto-alveolar conditions
J84.01Alveolar proteinosis
J84.02Pulmonary alveolar microlithiasis
J84.03Idiopathic pulmonary hemosiderosis
› Essential brown induration of lung
Code First: underlying disease, such as:
› disorders of iron metabolism (E83.1-)
Excludes 1: acute idiopathic pulmonary hemorrhage in infants [AIPHI] (R04.81)
J84.09Other alveolar and parieto-alveolar conditions
J84.1Other interstitial pulmonary diseases with fibrosis
Excludes 1: pulmonary fibrosis (chronic) due to inhalation of chemicals, gases, fumes or vapors (J68.4)
› pulmonary fibrosis (chronic) following radiation (J70.1)
J84.10Pulmonary fibrosis, unspecified
› Capillary fibrosis of lung
› Cirrhosis of lung (chronic) NOS
› Fibrosis of lung (atrophic) (chronic) (confluent) (massive) (perialveolar) (peribronchial) NOS
› Induration of lung (chronic) NOS
› Postinflammatory pulmonary fibrosis
J84.11Idiopathic interstitial pneumonia
Excludes 1: lymphoid interstitial pneumonia (J84.2)
› pneumocystis pneumonia (B59)
J84.111Idiopathic interstitial pneumonia, not otherwise specified
J84.112Idiopathic pulmonary fibrosis
› Cryptogenic fibrosing alveolitis
› Idiopathic fibrosing alveolitis
J84.113Idiopathic non-specific interstitial pneumonitis
Excludes 1: non-specific interstitial pneumonia NOS, or due to known underlying cause (J84.89)
J84.114Acute interstitial pneumonitis
› Hamman-Rich syndrome
Excludes 1: pneumocystis pneumonia (B59)
J84.115Respiratory bronchiolitis interstitial lung disease
J84.116Cryptogenic organizing pneumonia
Excludes 1: organizing pneumonia NOS, or due to known underlying cause (J84.89)
J84.117Desquamative interstitial pneumonia
J84.17Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
J84.170Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
› Progressive fibrotic interstitial lung disease
Code First: underlying disease, such as:
› lung diseases due to external agents (J60-J70)
› rheumatoid arthritis (M05.00-M06.9)
› sarcoidosis (D86.-)
› systemic connective tissue disorders (M30-M36)
J84.178Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
› Interstitial pneumonia (nonspecific) (usual) due to collagen vascular disease
› Interstitial pneumonia (nonspecific) (usual) in diseases classified elsewhere
› Organizing pneumonia due to collagen vascular disease
› Organizing pneumonia in diseases classified elsewhere
Code First: underlying disease, such as:
› progressive systemic sclerosis (M34.0)
› rheumatoid arthritis (M05.00-M06.9)
› systemic lupus erythematosis (M32.0-M32.9)
J84.2Lymphoid interstitial pneumonia
› Lymphoid interstitial pneumonitis
J84.8Other specified interstitial pulmonary diseases
Excludes 1: exogenous lipoid pneumonia (J69.1)
› unspecified lipoid pneumonia (J69.1)
J84.81Lymphangioleiomyomatosis
› Lymphangiomyomatosis
J84.82Adult pulmonary Langerhans cell histiocytosis
› Adult PLCH
J84.83Surfactant mutations of the lung
J84.84Other interstitial lung diseases of childhood
J84.841Neuroendocrine cell hyperplasia of infancy
J84.842Pulmonary interstitial glycogenosis
J84.843Alveolar capillary dysplasia with vein misalignment
J84.848Other interstitial lung diseases of childhood
J84.89Other specified interstitial pulmonary diseases
› Endogenous lipoid pneumonia
› Interstitial pneumonitis
› Non-specific interstitial pneumonitis NOS
› Organizing pneumonia NOS
Code First: , if applicable:
› poisoning due to drug or toxin (T51-T65 with fifth or sixth character to indicate intent), for toxic pneumonopathy
› underlying cause of pneumonopathy, if known
Use Additional Code: code, for adverse effect, to identify drug (T36-T50 with fifth or sixth character 5), if drug-induced
Excludes 1: cryptogenic organizing pneumonia (J84.116)
› idiopathic non-specific interstitial pneumonitis (J84.113)
› lipoid pneumonia, exogenous or unspecified (J69.1)
› lymphoid interstitial pneumonia (J84.2)
J84.9Interstitial pulmonary disease, unspecified
› Interstitial pneumonia NOS