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List of Diseases and Injuries

Viral and prion infections of the central nervous system (A80-A89)


Excludes 1: postpolio syndrome (G14)
sequelae of poliomyelitis (B91)
sequelae of viral encephalitis (B94.1)

A80Acute poliomyelitis
Excludes 1: acute flaccid myelitis (G04.82)

A80.0Acute paralytic poliomyelitis, vaccine-associated

A80.1Acute paralytic poliomyelitis, wild virus, imported

A80.2Acute paralytic poliomyelitis, wild virus, indigenous

A80.3Acute paralytic poliomyelitis, other and unspecified

A80.30Acute paralytic poliomyelitis, unspecified

A80.39Other acute paralytic poliomyelitis

A80.4Acute nonparalytic poliomyelitis

A80.9Acute poliomyelitis, unspecified

A81Atypical virus infections of central nervous system
Includes: diseases of the central nervous system caused by prions

Use Additional Code: code, if applicable, to identify:
dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
mild neurocognitive disorder due to known physiological condition (F06.7-)

A81.0Creutzfeldt-Jakob disease

A81.00Creutzfeldt-Jakob disease, unspecified
Jakob-Creutzfeldt disease, unspecified

A81.01Variant Creutzfeldt-Jakob disease
vCJD

A81.09Other Creutzfeldt-Jakob disease
CJD
Familial Creutzfeldt-Jakob disease
Iatrogenic Creutzfeldt-Jakob disease
Sporadic Creutzfeldt-Jakob disease
Subacute spongiform encephalopathy (with dementia)

A81.1Subacute sclerosing panencephalitis
Dawson's inclusion body encephalitis
Van Bogaert's sclerosing leukoencephalopathy

A81.2Progressive multifocal leukoencephalopathy
Multifocal leukoencephalopathy NOS

A81.8Other atypical virus infections of central nervous system

A81.81Kuru

A81.82Gerstmann-Sträussler-Scheinker syndrome
GSS syndrome

A81.83Fatal familial insomnia
FFI

A81.89Other atypical virus infections of central nervous system

A81.9Atypical virus infection of central nervous system, unspecified
Prion diseases of the central nervous system NOS

A82Rabies

A82.0Sylvatic rabies

A82.1Urban rabies

A82.9Rabies, unspecified

A83Mosquito-borne viral encephalitis
Includes: mosquito-borne viral meningoencephalitis

Excludes 2: Venezuelan equine encephalitis (A92.2)
West Nile fever (A92.3-)
West Nile virus (A92.3-)

A83.0Japanese encephalitis

A83.1Western equine encephalitis

A83.2Eastern equine encephalitis

A83.3St Louis encephalitis

A83.4Australian encephalitis
Kunjin virus disease

A83.5California encephalitis
California meningoencephalitis
La Crosse encephalitis

A83.6Rocio virus disease

A83.8Other mosquito-borne viral encephalitis

A83.9Mosquito-borne viral encephalitis, unspecified

A84Tick-borne viral encephalitis
Includes: tick-borne viral meningoencephalitis

A84.0Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis]

A84.1Central European tick-borne encephalitis

A84.8Other tick-borne viral encephalitis

A84.81Powassan virus disease

A84.89Other tick-borne viral encephalitis
Louping ill

Code First: , if applicable, transfusion related infection (T80.22-)

A84.9Tick-borne viral encephalitis, unspecified

A85Other viral encephalitis, not elsewhere classified
Includes: specified viral encephalomyelitis NEC
specified viral meningoencephalitis NEC

Excludes 1: encephalitis due to cytomegalovirus (B25.8)
encephalitis due to herpesvirus NEC (B10.0-)
encephalitis due to herpesvirus [herpes simplex] (B00.4)
encephalitis due to measles virus (B05.0)
encephalitis due to mumps virus (B26.2)
encephalitis due to poliomyelitis virus (A80.-)
encephalitis due to zoster (B02.0)
lymphocytic choriomeningitis (A87.2)
myalgic encephalomyelitis (G93.32)

A85.0Enteroviral encephalitis
Enteroviral encephalomyelitis

A85.1Adenoviral encephalitis
Adenoviral meningoencephalitis

A85.2Arthropod-borne viral encephalitis, unspecified
Excludes 1: West nile virus with encephalitis (A92.31)

A85.8Other specified viral encephalitis
Encephalitis lethargica
Von Economo-Cruchet disease

A86Unspecified viral encephalitis
Viral encephalomyelitis NOS
Viral meningoencephalitis NOS

A87Viral meningitis
Excludes 1: meningitis due to herpesvirus [herpes simplex] (B00.3)
meningitis due to herpesvirus [herpes simplex] (B00.3)
meningitis due to measles virus (B05.1)
meningitis due to mumps virus (B26.1)
meningitis due to poliomyelitis virus (A80.-)
meningitis due to zoster (B02.1)

A87.0Enteroviral meningitis
Coxsackievirus meningitis
Echovirus meningitis

A87.1Adenoviral meningitis

A87.2Lymphocytic choriomeningitis
Lymphocytic meningoencephalitis

A87.8Other viral meningitis

A87.9Viral meningitis, unspecified

A88Other viral infections of central nervous system, not elsewhere classified
Excludes 1: viral encephalitis NOS (A86)
viral meningitis NOS (A87.9)

A88.0Enteroviral exanthematous fever [Boston exanthem]

A88.1Epidemic vertigo

A88.8Other specified viral infections of central nervous system

A89Unspecified viral infection of central nervous system