Diseases of myoneural junction and muscle (G70-G73)
G70Myasthenia gravis and other myoneural disorders
Excludes 1: botulism (A05.1, A48.51-A48.52)
› transient neonatal myasthenia gravis (P94.0)
G70.0Myasthenia gravis
G70.00Myasthenia gravis without (acute) exacerbation
› Myasthenia gravis NOS
G70.01Myasthenia gravis with (acute) exacerbation
› Myasthenia gravis in crisis
G70.1Toxic myoneural disorders
Code First: (T51-T65) to identify toxic agent
G70.2Congenital and developmental myasthenia
G70.8Other specified myoneural disorders
G70.80Lambert-Eaton syndrome, unspecified
› Lambert-Eaton syndrome NOS
G70.81Lambert-Eaton syndrome in disease classified elsewhere
Code First: underlying disease
Excludes 1: Lambert-Eaton syndrome in neoplastic disease (G73.1)
G70.89Other specified myoneural disorders
G70.9Myoneural disorder, unspecified
G71Primary disorders of muscles
Excludes 2: arthrogryposis multiplex congenita (Q74.3)
› metabolic disorders (E70-E88)
› myositis (M60.-)
G71.0Muscular dystrophy
G71.00Muscular dystrophy, unspecified
G71.01Duchenne or Becker muscular dystrophy
› Autosomal recessive, childhood type, muscular dystrophy resembling Duchenne or Becker muscular dystrophy
› Benign [Becker] muscular dystrophy
› Severe [Duchenne] muscular dystrophy
G71.02Facioscapulohumeral muscular dystrophy
› Scapulohumeral muscular dystrophy
G71.03Limb girdle muscular dystrophies
G71.031Autosomal dominant limb girdle muscular dystrophy
› LGMD D4 calpain-3-related
› LGMD D5 collagen 6-related
› Limb girdle muscular dystrophy type 1
G71.032Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
› Limb girdle muscular dystrophy type 2A
› LGMD R1 calpain-3-related
› Primary calpainopathy
G71.033Limb girdle muscular dystrophy due to dysferlin dysfunction
› Dysferlinopathy
› LGMD R2 dysferlin-related
› Limb girdle muscular dystrophy type 2B
› Miyoshi Myopathy type 1
G71.034Limb girdle muscular dystrophy due to sarcoglycan dysfunction
G71.0340Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified
› Sarcoglycanopathy, NOS
G71.0341Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
› Alpha sarcoglycanopathy
› Limb-girdle muscular dystrophy due to alpha-sarcoglycan deficiency
› Limb girdle muscular dystrophy type 2D
G71.0342Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
› Beta sarcoglycanopathy
› Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
› Limb girdle muscular dystrophy type 2E
G71.0349Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
› Delta sarcoglycanopathy
› Delta-sarcoglycan-related LGMD R6
› Gamma sarcoglycanopathy
› Gamma-sarcoglycan-related LGMD R5
› Limb girdle muscular dystrophy type 2C
› Limb girdle muscular dystrophy type 2F
G71.035Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
› Anoctamin-5-related LGMD R12
› Anoctaminopathy
› Autosomal recessive limb girdle muscular dystrophy type 2L
› Miyoshi myopathy type 3
G71.038Other limb girdle muscular dystrophy
› LGMD R9 FKRP-related
› LGMD R22 collagen 6-related
› Limb girdle muscular dystrophy due to fukutin related protein dysfunction
› Limb girdle muscular dystrophy type 2I
› Other autosomal recessive limb girdle muscular dystrophy
G71.039Limb girdle muscular dystrophy, unspecified
G71.09Other specified muscular dystrophies
› Benign scapuloperoneal muscular dystrophy with early contractures [Emery-Dreifuss]
› Congenital muscular dystrophy NOS
› Congenital muscular dystrophy with specific morphological abnormalities of the muscle fiber
› Distal muscular dystrophy
› Ocular muscular dystrophy
› Oculopharyngeal muscular dystrophy
› Scapuloperoneal muscular dystrophy
G71.1Myotonic disorders
G71.11Myotonic muscular dystrophy
› Dystrophia myotonica [Steinert]
› Myotonia atrophica
› Myotonic dystrophy
› Proximal myotonic myopathy (PROMM)
› Steinert disease
G71.12Myotonia congenita
› Acetazolamide responsive myotonia congenita
› Dominant myotonia congenita [Thomsen disease]
› Myotonia levior
› Recessive myotonia congenita [Becker disease]
G71.13Myotonic chondrodystrophy
› Chondrodystrophic myotonia
› Congenital myotonic chondrodystrophy
› Schwartz-Jampel disease
G71.14Drug induced myotonia
Use Additional Code: code for adverse effect, if applicable, to identify drug (T36-T50) with fifth or sixth character 5)
G71.19Other specified myotonic disorders
› Myotonia fluctuans
› Myotonia permanens
› Neuromyotonia [Isaacs]
› Paramyotonia congenita (of von Eulenburg)
› Pseudomyotonia
› Symptomatic myotonia
G71.2Congenital myopathies
Excludes 2: arthrogryposis multiplex congenita (Q74.3)
G71.20Congenital myopathy, unspecified
G71.21Nemaline myopathy
G71.22Centronuclear myopathy
G71.220X-linked myotubular myopathy
› Myotubular (centronuclear) myopathy
G71.228Other centronuclear myopathy
› Autosomal centronuclear myopathy
› Autosomal dominant centronuclear myopathy
› Autosomal recessive centronuclear myopathy
› Centronuclear myopathy, NOS
G71.29Other congenital myopathy
› Central core disease
› Minicore disease
› Multicore disease
› Multiminicore disease
G71.3Mitochondrial myopathy, not elsewhere classified
Excludes 1: Kearns-Sayre syndrome (H49.81)
› Leber's disease (H47.21)
› Leigh's encephalopathy (G31.82)
› mitochondrial metabolism disorders (E88.4.-)
› Reye's syndrome (G93.7)
G71.8Other primary disorders of muscles
G71.9Primary disorder of muscle, unspecified
› Hereditary myopathy NOS
G72Other and unspecified myopathies
Excludes 1: arthrogryposis multiplex congenita (Q74.3)
› dermatopolymyositis (M33.-)
› ischemic infarction of muscle (M62.2-)
› myositis (M60.-)
› polymyositis (M33.2.-)
G72.0Drug-induced myopathy
Use Additional Code: code for adverse effect, if applicable, to identify drug (T36-T50) with fifth or sixth character 5)
G72.1Alcoholic myopathy
Use Additional Code: code to identify alcoholism (F10.-)
G72.2Myopathy due to other toxic agents
Code First: (T51-T65) to identify toxic agent
G72.3Periodic paralysis
› Familial periodic paralysis
› Hyperkalemic periodic paralysis (familial)
› Hypokalemic periodic paralysis (familial)
› Myotonic periodic paralysis (familial)
› Normokalemic paralysis (familial)
› Potassium sensitive periodic paralysis
Excludes 1: paramyotonia congenita (of von Eulenburg) (G71.19)
G72.4Inflammatory and immune myopathies, not elsewhere classified
G72.41Inclusion body myositis [IBM]
G72.49Other inflammatory and immune myopathies, not elsewhere classified
› Inflammatory myopathy NOS
G72.8Other specified myopathies
G72.81Critical illness myopathy
› Acute necrotizing myopathy
› Acute quadriplegic myopathy
› Intensive care (ICU) myopathy
› Myopathy of critical illness
G72.89Other specified myopathies
G72.9Myopathy, unspecified
G73Disorders of myoneural junction and muscle in diseases classified elsewhere
G73.1Lambert-Eaton syndrome in neoplastic disease
Code First: underlying neoplasm (C00-D49)
Excludes 1: Lambert-Eaton syndrome not associated with neoplasm (G70.80-G70.81)
G73.3Myasthenic syndromes in other diseases classified elsewhere
Code First: underlying disease, such as:
› neoplasm (C00-D49)
› thyrotoxicosis (E05.-)
G73.7Myopathy in diseases classified elsewhere
Code First: underlying disease, such as:
› glycogen storage disease (E74.0-)
› hyperparathyroidism (E21.0, E21.3)
› hypoparathyroidism (E20.-)
› lipid storage disorders (E75.-)
Excludes 1: myopathy in:
› rheumatoid arthritis (M05.32)
› sarcoidosis (D86.87)
› scleroderma (M34.82)
› Sjögren syndrome (M35.03)
› systemic lupus erythematosus (M32.19)