section name header

List of Diseases and Injuries

Other forms of heart disease (I30-I5A)

I30Acute pericarditis
Includes: acute mediastinopericarditis
› acute myopericarditis
› acute pericardial effusion
› acute pleuropericarditis
› acute pneumopericarditis

Excludes 1: Dressler's syndrome (I24.1)
› rheumatic pericarditis (acute) (I01.0)
› viral pericarditis due to Coxsakie virus (B33.23)

I30.0Acute nonspecific idiopathic pericarditis

I30.1Infective pericarditis
› Pneumococcal pericarditis
› Pneumopyopericardium
› Purulent pericarditis
› Pyopericarditis
› Pyopericardium
› Pyopneumopericardium
› Staphylococcal pericarditis
› Streptococcal pericarditis
› Suppurative pericarditis
› Viral pericarditis

Use Additional Code: code (B95-B97) to identify infectious agent

I30.8Other forms of acute pericarditis

I30.9Acute pericarditis, unspecified

I31Other diseases of pericardium
Excludes 1: diseases of pericardium specified as rheumatic (I09.2)
› postcardiotomy syndrome (I97.0)
› traumatic injury to pericardium (S26.-)

I31.0Chronic adhesive pericarditis
› Accretio cordis
› Adherent pericardium
› Adhesive mediastinopericarditis

I31.1Chronic constrictive pericarditis
› Concretio cordis
› Pericardial calcification

I31.2Hemopericardium, not elsewhere classified
Excludes 1: hemopericardium as current complication following acute myocardial infarction (I23.0)
› malignant pericardial effusion (I31.31)

I31.3Pericardial effusion (noninflammatory)
Excludes 1: acute pericardial effusion (I30.9)

I31.31Malignant pericardial effusion in diseases classified elsewhere
Code First: underlying neoplasm (C00-D49)

I31.39Other pericardial effusion (noninflammatory)
› Chylopericardium

I31.4Cardiac tamponade
Code First: underlying cause

I31.8Other specified diseases of pericardium
› Epicardial plaques
› Focal pericardial adhesions

I31.9Disease of pericardium, unspecified
› Pericarditis (chronic) NOS

I32Pericarditis in diseases classified elsewhere
Code First: underlying disease

Excludes 1: pericarditis (in):
› coxsackie (virus) (B33.23)
› gonococcal (A54.83)
› meningococcal (A39.53)
› rheumatoid (arthritis) (M05.31)
› syphilitic (A52.06)
› systemic lupus erythematosus (M32.12)
› tuberculosis (A18.84)

I33Acute and subacute endocarditis
Excludes 1: acute rheumatic endocarditis (I01.1)
› endocarditis NOS (I38)

I33.0Acute and subacute infective endocarditis
› Bacterial endocarditis (acute) (subacute)
› Infective endocarditis (acute) (subacute) NOS
› Endocarditis lenta (acute) (subacute)
› Malignant endocarditis (acute) (subacute)
› Purulent endocarditis (acute) (subacute)
› Septic endocarditis (acute) (subacute)
› Ulcerative endocarditis (acute) (subacute)
› Vegetative endocarditis (acute) (subacute)

Use Additional Code: code (B95-B97) to identify infectious agent

I33.9Acute and subacute endocarditis, unspecified
› Acute endocarditis NOS
› Acute myoendocarditis NOS
› Acute periendocarditis NOS
› Subacute endocarditis NOS
› Subacute myoendocarditis NOS
› Subacute periendocarditis NOS

I34Nonrheumatic mitral valve disorders
Excludes 1: mitral valve disease (I05.9)
› mitral valve failure (I05.8)
› mitral valve stenosis (I05.0)
› mitral valve disorder of unspecified cause with diseases of aortic and/or tricuspid valve(s) (I08.-)
› mitral valve disorder of unspecified cause with mitral stenosis or obstruction (I05.0)
› mitral valve disorder specified as congenital (Q23.2, Q23.9)
› mitral valve disorder specified as rheumatic (I05.-)

I34.0Nonrheumatic mitral (valve) insufficiency
› Nonrheumatic mitral (valve) incompetence NOS
› Nonrheumatic mitral (valve) regurgitation NOS

Code Also: , if applicable:
› nonrheumatic mitral (valve) annulus calcification (I34.81)

I34.1Nonrheumatic mitral (valve) prolapse
› Floppy nonrheumatic mitral valve syndrome

Excludes 1: Marfan's syndrome (Q87.4-)

I34.2Nonrheumatic mitral (valve) stenosis
Code Also: , if applicable:
› nonrheumatic mitral (valve) annulus calcification (I34.81)

I34.8Other nonrheumatic mitral valve disorders

I34.81Nonrheumatic mitral (valve) annulus calcification
› Nonrheumatic mitral (valve) annular calcification
› Mitral (valve) annulus calcification NOS

Code Also: , if applicable:
› nonrheumatic mitral (valve) insufficiency (I34.0)
› nonrheumatic mitral (valve) stenosis (I34.2)

I34.89Other nonrheumatic mitral valve disorders

I34.9Nonrheumatic mitral valve disorder, unspecified

I35Nonrheumatic aortic valve disorders
Excludes 1: aortic valve disorder of unspecified cause but with diseases of mitral and/or tricuspid valve(s) (I08.-)
› aortic valve disorder specified as congenital (Q23.0, Q23.1)
› aortic valve disorder specified as rheumatic (I06.-)
› hypertrophic subaortic stenosis (I42.1)

I35.0Nonrheumatic aortic (valve) stenosis

I35.1Nonrheumatic aortic (valve) insufficiency
› Nonrheumatic aortic (valve) incompetence NOS
› Nonrheumatic aortic (valve) regurgitation NOS

I35.2Nonrheumatic aortic (valve) stenosis with insufficiency

I35.8Other nonrheumatic aortic valve disorders

I35.9Nonrheumatic aortic valve disorder, unspecified

I36Nonrheumatic tricuspid valve disorders
Excludes 1: tricuspid valve disorders of unspecified cause (I07.-)
› tricuspid valve disorders specified as congenital (Q22.4, Q22.8, Q22.9)
› tricuspid valve disorders specified as rheumatic (I07.-)
› tricuspid valve disorders with aortic and/or mitral valve involvement (I08.-)

I36.0Nonrheumatic tricuspid (valve) stenosis

I36.1Nonrheumatic tricuspid (valve) insufficiency
› Nonrheumatic tricuspid (valve) incompetence
› Nonrheumatic tricuspid (valve) regurgitation

I36.2Nonrheumatic tricuspid (valve) stenosis with insufficiency

I36.8Other nonrheumatic tricuspid valve disorders

I36.9Nonrheumatic tricuspid valve disorder, unspecified

I37Nonrheumatic pulmonary valve disorders
Excludes 1: pulmonary valve disorder specified as congenital (Q22.1, Q22.2, Q22.3)
› pulmonary valve disorder specified as rheumatic (I09.89)

I37.0Nonrheumatic pulmonary valve stenosis

I37.1Nonrheumatic pulmonary valve insufficiency
› Nonrheumatic pulmonary valve incompetence
› Nonrheumatic pulmonary valve regurgitation

I37.2Nonrheumatic pulmonary valve stenosis with insufficiency

I37.8Other nonrheumatic pulmonary valve disorders

I37.9Nonrheumatic pulmonary valve disorder, unspecified

I38Endocarditis, valve unspecified
Includes: endocarditis (chronic) NOS
› valvular incompetence NOS
› valvular insufficiency NOS
› valvular regurgitation NOS
› valvular stenosis NOS
› valvulitis (chronic) NOS

Excludes 1: congenital insufficiency of cardiac valve NOS (Q24.8)
› congenital stenosis of cardiac valve NOS (Q24.8)
› endocardial fibroelastosis (I42.4)
› endocarditis specified as rheumatic (I09.1)

I39Endocarditis and heart valve disorders in diseases classified elsewhere
Code First: underlying disease, such as:
› Q fever (A78)

Excludes 1: endocardial involvement in:
› candidiasis (B37.6)
› gonococcal infection (A54.83)
› Libman-Sacks disease (M32.11)
› listerosis (A32.82)
› meningococcal infection (A39.51)
› rheumatoid arthritis (M05.31)
› syphilis (A52.03)
› tuberculosis (A18.84)
› typhoid fever (A01.02)

I40Acute myocarditis
Includes: subacute myocarditis

Excludes 1: acute rheumatic myocarditis (I01.2)

I40.0Infective myocarditis
› Septic myocarditis

Use Additional Code: code (B95-B97) to identify infectious agent

I40.1Isolated myocarditis
› Fiedler's myocarditis
› Giant cell myocarditis
› Idiopathic myocarditis

I40.8Other acute myocarditis

I40.9Acute myocarditis, unspecified

I41Myocarditis in diseases classified elsewhere
Code First: underlying disease, such as:
› typhus (A75.0-A75.9)

Excludes 1: myocarditis (in):
› Chagas' disease (chronic) (B57.2)
› acute (B57.0)
› coxsackie (virus) infection (B33.22)
› diphtheritic (A36.81)
› gonococcal (A54.83)
› influenzal (J09.X9, J10.82, J11.82)
› meningococcal (A39.52)
› mumps (B26.82)
› rheumatoid arthritis (M05.31)
› sarcoid (D86.85)
› syphilis (A52.06)
› toxoplasmosis (B58.81)
› tuberculous (A18.84)

I42Cardiomyopathy
Includes: myocardiopathy

Code First: pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4)

Excludes 2: ischemic cardiomyopathy (I25.5)
› peripartum cardiomyopathy (O90.3)
› ventricular hypertrophy (I51.7)

I42.0Dilated cardiomyopathy
› Congestive cardiomyopathy

I42.1Obstructive hypertrophic cardiomyopathy
› Hypertrophic subaortic stenosis (idiopathic)

I42.2Other hypertrophic cardiomyopathy
› Nonobstructive hypertrophic cardiomyopathy

I42.3Endomyocardial (eosinophilic) disease
› Endomyocardial (tropical) fibrosis
› Löffler's endocarditis

I42.4Endocardial fibroelastosis
› Congenital cardiomyopathy
› Elastomyofibrosis

I42.5Other restrictive cardiomyopathy
› Constrictive cardiomyopathy NOS

I42.6Alcoholic cardiomyopathy
Code Also: presence of alcoholism (F10.-)

I42.7Cardiomyopathy due to drug and external agent
Code First: poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4)

Use Additional Code: code for adverse effect, if applicable, to identify drug (T36-T50) with fifth or sixth character 5)

I42.8Other cardiomyopathies

I42.9Cardiomyopathy, unspecified
› Cardiomyopathy (primary) (secondary) NOS

I43Cardiomyopathy in diseases classified elsewhere
Code First: underlying disease, such as:
› amyloidosis (E85.-)
› glycogen storage disease (E74.0-)
› gout (M10.0-)
› thyrotoxicosis (E05.0-E05.9-)

Excludes 1: cardiomyopathy (in):
› coxsackie (virus) (B33.24)
› diphtheria (A36.81)
› sarcoidosis (D86.85)
› tuberculosis (A18.84)

I44Atrioventricular and left bundle-branch block

I44.0Atrioventricular block, first degree

I44.1Atrioventricular block, second degree
› Atrioventricular block, type I and II
› Möbitz block, type I and II
› Second degree block, type I and II
› Wenckebach's block

I44.2Atrioventricular block, complete
› Complete heart block NOS
› Third degree block

I44.3Other and unspecified atrioventricular block
› Atrioventricular block NOS

I44.30Unspecified atrioventricular block

I44.39Other atrioventricular block

I44.4Left anterior fascicular block

I44.5Left posterior fascicular block

I44.6Other and unspecified fascicular block

I44.60Unspecified fascicular block
› Left bundle-branch hemiblock NOS

I44.69Other fascicular block

I44.7Left bundle-branch block, unspecified

I45Other conduction disorders

I45.0Right fascicular block

I45.1Other and unspecified right bundle-branch block

I45.10Unspecified right bundle-branch block
› Right bundle-branch block NOS

I45.19Other right bundle-branch block

I45.2Bifascicular block

I45.3Trifascicular block

I45.4Nonspecific intraventricular block
› Bundle-branch block NOS

I45.5Other specified heart block
› Sinoatrial block
› Sinoauricular block

Excludes 1: heart block NOS (I45.9)

I45.6Pre-excitation syndrome
› Accelerated atrioventricular conduction
› Accessory atrioventricular conduction
› Anomalous atrioventricular excitation
› Lown-Ganong-Levine syndrome
› Pre-excitation atrioventricular conduction
› Wolff-Parkinson-White syndrome

I45.8Other specified conduction disorders

I45.81Long QT syndrome

I45.89Other specified conduction disorders
› Atrioventricular [AV] dissociation
› Interference dissociation
› Isorhythmic dissociation
› Nonparoxysmal AV nodal tachycardia

I45.9Conduction disorder, unspecified
› Heart block NOS
› Stokes-Adams syndrome

I46Cardiac arrest
Excludes 2: cardiogenic shock (R57.0)

I46.2Cardiac arrest due to underlying cardiac condition
Code First: underlying cardiac condition

I46.8Cardiac arrest due to other underlying condition
Code First: underlying condition

I46.9Cardiac arrest, cause unspecified

I47Paroxysmal tachycardia
Code First: tachycardia complicating:
› abortion or ectopic or molar pregnancy (O00-O07, O08.8)
› obstetric surgery and procedures (O75.4)

Excludes 1: tachycardia NOS (R00.0)
› sinoauricular tachycardia NOS (R00.0)
› sinus [sinusal] tachycardia NOS (R00.0)

I47.0Re-entry ventricular arrhythmia

I47.1Supraventricular tachycardia

I47.10Supraventricular tachycardia, unspecified

I47.11Inappropriate sinus tachycardia, so stated
› IST

I47.19Other supraventricular tachycardia
› Atrial (paroxysmal) tachycardia
› Atrioventricular [AV] (paroxysmal) tachycardia
› Atrioventricular re-entrant (nodal) tachycardia [AVNRT] [AVRT]
› Junctional (paroxysmal) tachycardia
› Nodal (paroxysmal) tachycardia

I47.2Ventricular tachycardia

I47.20Ventricular tachycardia, unspecified

I47.21Torsades de pointes
Code Also: , if applicable, long QT syndrome (I45.81)

Use Additional Code: code for adverse effect, if applicable, to identify drug (T36-T50) with fifth or sixth character 5)

I47.29Other ventricular tachycardia

I47.9Paroxysmal tachycardia, unspecified
› Bouveret (-Hoffman) syndrome

I48Atrial fibrillation and flutter

I48.0Paroxysmal atrial fibrillation

I48.1Persistent atrial fibrillation
Excludes 1: Permanent atrial fibrillation (I48.21)

I48.11Longstanding persistent atrial fibrillation

I48.19Other persistent atrial fibrillation
› Chronic persistent atrial fibrillation
› Persistent atrial fibrillation, NOS

I48.2Chronic atrial fibrillation

I48.20Chronic atrial fibrillation, unspecified
Excludes 1: Chronic persistent atrial fibrillation (I48.19)

I48.21Permanent atrial fibrillation

I48.3Typical atrial flutter
› Type I atrial flutter

I48.4Atypical atrial flutter
› Type II atrial flutter

I48.9Unspecified atrial fibrillation and atrial flutter

I48.91Unspecified atrial fibrillation

I48.92Unspecified atrial flutter

I49Other cardiac arrhythmias
Code First: cardiac arrhythmia complicating:
› abortion or ectopic or molar pregnancy (O00-O07, O08.8)
› obstetric surgery and procedures (O75.4)

Excludes 2: bradycardia NOS (R00.1)
› neonatal dysrhythmia (P29.1-)
› sinoatrial bradycardia (R00.1)
› sinus bradycardia (R00.1)
› vagal bradycardia (R00.1)

I49.0Ventricular fibrillation and flutter

I49.01Ventricular fibrillation

I49.02Ventricular flutter

I49.1Atrial premature depolarization
› Atrial premature beats

I49.2Junctional premature depolarization

I49.3Ventricular premature depolarization

I49.4Other and unspecified premature depolarization

I49.40Unspecified premature depolarization
› Premature beats NOS

I49.49Other premature depolarization
› Ectopic beats
› Extrasystoles
› Extrasystolic arrhythmias
› Premature contractions

I49.5Sick sinus syndrome
› Tachycardia-bradycardia syndrome

I49.8Other specified cardiac arrhythmias
› Brugada syndrome
› Coronary sinus rhythm disorder
› Ectopic rhythm disorder
› Nodal rhythm disorder

I49.9Cardiac arrhythmia, unspecified
› Arrhythmia (cardiac) NOS

I50Heart failure
Code First: heart failure complicating abortion or ectopic or molar pregnancy (O00-O07, O08.8)
› heart failure due to hypertension (I11.0)
› heart failure due to hypertension with chronic kidney disease (I13.-)
› heart failure following surgery (I97.13-)
› obstetric surgery and procedures (O75.4)
› rheumatic heart failure (I09.81)

Excludes 2: cardiac arrest (I46.-)
› neonatal cardiac failure (P29.0)

I50.1Left ventricular failure, unspecified
› Cardiac asthma
› Edema of lung with heart disease NOS
› Edema of lung with heart failure
› Left heart failure
› Pulmonary edema with heart disease NOS
› Pulmonary edema with heart failure

Excludes 1: edema of lung without heart disease or heart failure (J81.-)
› pulmonary edema without heart disease or failure (J81.-)

I50.2Systolic (congestive) heart failure
› Heart failure with reduced ejection fraction [HFrEF]
› Systolic left ventricular heart failure

Code Also: end stage heart failure, if applicable (I50.84)

Excludes 1: combined systolic (congestive) and diastolic (congestive) heart failure (I50.4-)

I50.20Unspecified systolic (congestive) heart failure

I50.21Acute systolic (congestive) heart failure

I50.22Chronic systolic (congestive) heart failure

I50.23Acute on chronic systolic (congestive) heart failure

I50.3Diastolic (congestive) heart failure
› Diastolic left ventricular heart failure
› Heart failure with normal ejection fraction
› Heart failure with preserved ejection fraction [HFpEF]

Code Also: end stage heart failure, if applicable (I50.84)

Excludes 1: combined systolic (congestive) and diastolic (congestive) heart failure (I50.4-)

I50.30Unspecified diastolic (congestive) heart failure

I50.31Acute diastolic (congestive) heart failure

I50.32Chronic diastolic (congestive) heart failure

I50.33Acute on chronic diastolic (congestive) heart failure

I50.4Combined systolic (congestive) and diastolic (congestive) heart failure
› Combined systolic and diastolic left ventricular heart failure
› Heart failure with reduced ejection fraction and diastolic dysfunction

Code Also: end stage heart failure, if applicable (I50.84)

I50.40Unspecified combined systolic (congestive) and diastolic (congestive) heart failure

I50.41Acute combined systolic (congestive) and diastolic (congestive) heart failure

I50.42Chronic combined systolic (congestive) and diastolic (congestive) heart failure

I50.43Acute on chronic combined systolic (congestive) and diastolic (congestive) heart failure

I50.8Other heart failure

I50.81Right heart failure
› Right ventricular failure

I50.810Right heart failure, unspecified
› Right heart failure without mention of left heart failure
› Right ventricular failure NOS

I50.811Acute right heart failure
› Acute isolated right heart failure
› Acute (isolated) right ventricular failure

I50.812Chronic right heart failure
› Chronic isolated right heart failure
› Chronic (isolated) right ventricular failure

I50.813Acute on chronic right heart failure
› Acute on chronic isolated right heart failure
› Acute on chronic (isolated) right ventricular failure
› Acute decompensation of chronic (isolated) right ventricular failure
› Acute exacerbation of chronic (isolated) right ventricular failure

I50.814Right heart failure due to left heart failure
› Right ventricular failure secondary to left ventricular failure

Code Also: the type of left ventricular failure, if known (I50.2-I50.43)

Excludes 1: Right heart failure with but not due to left heart failure (I50.82)

I50.82Biventricular heart failure
Code Also: the type of left ventricular failure as systolic, diastolic, or combined, if known (I50.2-I50.43)

I50.83High output heart failure

I50.84End stage heart failure
› Stage D heart failure

Code Also: the type of heart failure as systolic, diastolic, or combined, if known (I50.2-I50.43)

I50.89Other heart failure

I50.9Heart failure, unspecified
› Cardiac, heart or myocardial failure NOS
› Congestive heart disease
› Congestive heart failure NOS

Excludes 2: fluid overload unrelated to congestive heart failure (E87.70)

I51Complications and ill-defined descriptions of heart disease
Excludes 1: any condition in I51.4-I51.9 due to hypertension (I11.-)
› any condition in I51.4-I51.9 due to hypertension and chronic kidney disease (I13.-)
› heart disease specified as rheumatic (I00-I09)

I51.0Cardiac septal defect, acquired
› Acquired septal atrial defect (old)
› Acquired septal auricular defect (old)
› Acquired septal ventricular defect (old)

Excludes 1: cardiac septal defect as current complication following acute myocardial infarction (I23.1, I23.2)

I51.1Rupture of chordae tendineae, not elsewhere classified
Excludes 1: rupture of chordae tendineae as current complication following acute myocardial infarction (I23.4)

I51.2Rupture of papillary muscle, not elsewhere classified
Excludes 1: rupture of papillary muscle as current complication following acute myocardial infarction (I23.5)

I51.3Intracardiac thrombosis, not elsewhere classified
› Apical thrombosis (old)
› Atrial thrombosis (old)
› Auricular thrombosis (old)
› Mural thrombosis (old)
› Ventricular thrombosis (old)

Excludes 1: intracardiac thrombosis as current complication following acute myocardial infarction (I23.6)

I51.4Myocarditis, unspecified
› Chronic (interstitial) myocarditis
› Myocardial fibrosis
› Myocarditis NOS

Excludes 1: acute or subacute myocarditis (I40.-)

I51.5Myocardial degeneration
› Fatty degeneration of heart or myocardium
› Myocardial disease
› Senile degeneration of heart or myocardium

I51.7Cardiomegaly
› Cardiac dilatation
› Cardiac hypertrophy
› Ventricular dilatation

I51.8Other ill-defined heart diseases

I51.81Takotsubo syndrome
› Reversible left ventricular dysfunction following sudden emotional stress
› Stress induced cardiomyopathy
› Takotsubo cardiomyopathy
› Transient left ventricular apical ballooning syndrome

I51.89Other ill-defined heart diseases
› Carditis (acute)(chronic)
› Pancarditis (acute)(chronic)

I51.9Heart disease, unspecified

I52Other heart disorders in diseases classified elsewhere
Code First: underlying disease, such as:
› congenital syphilis (A50.5)
› mucopolysaccharidosis (E76.3)
› schistosomiasis (B65.0-B65.9)

Excludes 1: heart disease (in):
› gonococcal infection (A54.83)
› meningococcal infection (A39.50)
› rheumatoid arthritis (M05.31)
› syphilis (A52.06)

I5ANon-ischemic myocardial injury (non-traumatic)
› Acute (non-ischemic) myocardial injury
› Chronic (non-ischemic) myocardial injury
› Unspecified (non-ischemic) myocardial injury

Code First: the underlying cause, if known and applicable, such as:
› acute kidney failure (N17.-)
› acute myocarditis (I40.-)
› cardiomyopathy (I42.-)
› chronic kidney disease (CKD) (N18.-)
› heart failure (I50.-)
› hypertensive urgency (I16.0)
› nonrheumatic aortic valve disorders (I35.-)
› paroxysmal tachycardia (I47.-)
› pulmonary embolism (I26.-)
› pulmonary hypertension (I27.0, I27.2-)
› sepsis (A41.-)
› takotsubo syndrome (I51.81)

Excludes 1: acute myocardial infarction (I21.-)
› injury of heart (S26.-)

Excludes 2: other acute ischemic heart diseases (I24.-)