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List of Diseases and Injuries

Demyelinating diseases of the central nervous system (G35-G37)

G35Multiple sclerosis

G35.ARelapsing-remitting multiple sclerosis
› Exclude1: demyelinating disease of central nervous system, unspecified (G37.9)

G35.BPrimary progressive multiple sclerosis

G35.B0Primary progressive multiple sclerosis, unspecified

G35.B1Active primary progressive multiple sclerosis
› Primary progressive multiple sclerosis with evidence of inflammatory disease activity

G35.B2Non-active primary progressive multiple sclerosis
› Primary progressive multiple sclerosis without evidence of inflammatory disease activity

G35.CSecondary progressive multiple sclerosis

G35.C0Secondary progressive multiple sclerosis, unspecified

G35.C1Active secondary progressive multiple sclerosis
› Secondary progressive multiple sclerosis with evidence of inflammatory disease activity

G35.C2Non-active secondary progressive multiple sclerosis
› Secondary progressive multiple sclerosis without evidence of inflammatory disease activity

G35.DMultiple sclerosis, unspecified
› Disseminated multiple sclerosis
› Generalized multiple sclerosis
› Multiple sclerosis NOS
› Multiple sclerosis of brain stem
› Multiple sclerosis of cord

G36Other acute disseminated demyelination
Excludes 1: postinfectious encephalitis and encephalomyelitis NOS (G04.01)

G36.0Neuromyelitis optica [Devic]
› Demyelination in optic neuritis

Excludes 1: optic neuritis NOS (H46)

G36.1Acute and subacute hemorrhagic leukoencephalitis [Hurst]

G36.8Other specified acute disseminated demyelination

G36.9Acute disseminated demyelination, unspecified

G37Other demyelinating diseases of central nervous system

G37.0Diffuse sclerosis of central nervous system
› Periaxial encephalitis
› Schilder's disease

Excludes 1: X linked adrenoleukodystrophy (E71.52-)

G37.1Central demyelination of corpus callosum

G37.2Central pontine myelinolysis

G37.3Acute transverse myelitis in demyelinating disease of central nervous system
› Acute transverse myelitis NOS
› Acute transverse myelopathy

Excludes 1: acute flaccid myelitis (G04.82)
› multiple sclerosis (G35-)
› neuromyelitis optica [Devic] (G36.0)

G37.4Subacute necrotizing myelitis of central nervous system

G37.5Concentric sclerosis [Balo] of central nervous system

G37.8Other specified demyelinating diseases of central nervous system

G37.81Myelin oligodendrocyte glycoprotein antibody disease
› MOG antibody disease

Code Also: associated manifestations, if known, such as:
› noninfectious acute disseminated encephalomyelitis (G04.81)
› neuromyelitis optica (G36.0)

G37.89Other specified demyelinating diseases of central nervous system

G37.9Demyelinating disease of central nervous system, unspecified
› Clinically isolated syndromes