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List of Diseases and Injuries

Demyelinating diseases of the central nervous system (G35-G37)

G35Multiple sclerosis

G35.ARelapsing-remitting multiple sclerosis
Exclude1: demyelinating disease of central nervous system, unspecified (G37.9)

G35.BPrimary progressive multiple sclerosis

G35.B0Primary progressive multiple sclerosis, unspecified

G35.B1Active primary progressive multiple sclerosis
Primary progressive multiple sclerosis with evidence of inflammatory disease activity

G35.B2Non-active primary progressive multiple sclerosis
Primary progressive multiple sclerosis without evidence of inflammatory disease activity

G35.CSecondary progressive multiple sclerosis

G35.C0Secondary progressive multiple sclerosis, unspecified

G35.C1Active secondary progressive multiple sclerosis
Secondary progressive multiple sclerosis with evidence of inflammatory disease activity

G35.C2Non-active secondary progressive multiple sclerosis
Secondary progressive multiple sclerosis without evidence of inflammatory disease activity

G35.DMultiple sclerosis, unspecified
Disseminated multiple sclerosis
Generalized multiple sclerosis
Multiple sclerosis NOS
Multiple sclerosis of brain stem
Multiple sclerosis of cord

G36Other acute disseminated demyelination
Excludes 1: postinfectious encephalitis and encephalomyelitis NOS (G04.01)

G36.0Neuromyelitis optica [Devic]
Demyelination in optic neuritis

Excludes 1: optic neuritis NOS (H46)

G36.1Acute and subacute hemorrhagic leukoencephalitis [Hurst]

G36.8Other specified acute disseminated demyelination

G36.9Acute disseminated demyelination, unspecified

G37Other demyelinating diseases of central nervous system

G37.0Diffuse sclerosis of central nervous system
Periaxial encephalitis
Schilder's disease

Excludes 1: X linked adrenoleukodystrophy (E71.52-)

G37.1Central demyelination of corpus callosum

G37.2Central pontine myelinolysis

G37.3Acute transverse myelitis in demyelinating disease of central nervous system
Acute transverse myelitis NOS
Acute transverse myelopathy

Excludes 1: acute flaccid myelitis (G04.82)
multiple sclerosis (G35-)
neuromyelitis optica [Devic] (G36.0)

G37.4Subacute necrotizing myelitis of central nervous system

G37.5Concentric sclerosis [Balo] of central nervous system

G37.8Other specified demyelinating diseases of central nervous system

G37.81Myelin oligodendrocyte glycoprotein antibody disease
MOG antibody disease

Code Also: associated manifestations, if known, such as:
noninfectious acute disseminated encephalomyelitis (G04.81)
neuromyelitis optica (G36.0)

G37.89Other specified demyelinating diseases of central nervous system

G37.9Demyelinating disease of central nervous system, unspecified
Clinically isolated syndromes