Glomerular diseases (N00-N08)
N00Acute nephritic syndrome
Includes: acute glomerular disease
› acute glomerulonephritis
› acute nephritis
Excludes 1: acute tubulo-interstitial nephritis (N10)
› nephritic syndrome NOS (N05.-)
N00.0Acute nephritic syndrome with minor glomerular abnormality
› Acute nephritic syndrome with minimal change lesion
N00.1Acute nephritic syndrome with focal and segmental glomerular lesions
› Acute nephritic syndrome with focal and segmental hyalinosis
› Acute nephritic syndrome with focal and segmental sclerosis
› Acute nephritic syndrome with focal glomerulonephritis
N00.2Acute nephritic syndrome with diffuse membranous glomerulonephritis
N00.3Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N00.4Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N00.5Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
Excludes 1: Acute nephritic syndrome with C3 glomerulonephritis (N00.A)
› Acute nephritic syndrome with C3 glomerulopathy (N00.A)
N00.6Acute nephritic syndrome with dense deposit disease
› Acute nephritic syndrome with C3 glomerulopathy with dense deposit disease
› Acute nephritic syndrome with membranoproliferative glomerulonephritis, type 2
N00.7Acute nephritic syndrome with diffuse crescentic glomerulonephritis
› Acute nephritic syndrome with extracapillary glomerulonephritis
N00.8Acute nephritic syndrome with other morphologic changes
› Acute nephritic syndrome with proliferative glomerulonephritis NOS
N00.9Acute nephritic syndrome with unspecified morphologic changes
N00.AAcute nephritic syndrome with C3 glomerulonephritis
› Acute nephritic syndrome with C3 glomerulopathy, NOS
Excludes 1: Acute nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N00.6)
N00.BAcute nephritic syndrome with immune complex membranoproliferative glomerulonephritis
N00.B1Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN)
N00.B2Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
N01Rapidly progressive nephritic syndrome
Includes: rapidly progressive glomerular disease
› rapidly progressive glomerulonephritis
› rapidly progressive nephritis
Excludes 1: nephritic syndrome NOS (N05.-)
N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
› Rapidly progressive nephritic syndrome with minimal change lesion
N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
› Rapidly progressive nephritic syndrome with focal and segmental hyalinosis
› Rapidly progressive nephritic syndrome with focal and segmental sclerosis
› Rapidly progressive nephritic syndrome with focal glomerulonephritis
N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
› Rapidly progressive nephritic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
Excludes 1: Rapidly progressive nephritic syndrome with C3 glomerulonephritis (N01.A)
› Rapidly progressive nephritic syndrome with C3 glomerulopathy (N01.A)
N01.6Rapidly progressive nephritic syndrome with dense deposit disease
› Rapidly progressive nephritic syndrome with C3 glomerulopathy with dense deposit disease
› Rapidly progressive nephritic syndrome with membranoproliferative glomerulonephritis, type 2
N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
› Rapidly progressive nephritic syndrome with extracapillary glomerulonephritis
N01.8Rapidly progressive nephritic syndrome with other morphologic changes
› Rapidly progressive nephritic syndrome with proliferative glomerulonephritis NOS
N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changes
N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis
› Rapidly progressive nephritic syndrome with C3 glomerulopathy, NOS
Excludes 1: Rapidly progressive nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N01.6)
N02Recurrent and persistent hematuria
Excludes 1: acute cystitis with hematuria (N30.01)
› hematuria NOS (R31.9)
› hematuria not associated with specified morphologic lesions (R31.-)
N02.0Recurrent and persistent hematuria with minor glomerular abnormality
› Recurrent and persistent hematuria with minimal change lesion
N02.1Recurrent and persistent hematuria with focal and segmental glomerular lesions
› Recurrent and persistent hematuria with focal and segmental hyalinosis
› Recurrent and persistent hematuria with focal and segmental sclerosis
› Recurrent and persistent hematuria with focal glomerulonephritis
N02.2Recurrent and persistent hematuria with diffuse membranous glomerulonephritis
N02.3Recurrent and persistent hematuria with diffuse mesangial proliferative glomerulonephritis
N02.4Recurrent and persistent hematuria with diffuse endocapillary proliferative glomerulonephritis
N02.5Recurrent and persistent hematuria with diffuse mesangiocapillary glomerulonephritis
› Recurrent and persistent hematuria with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
Excludes 1: Recurrent and persistent hematuria with C3 glomerulonephritis (N02.A)
› Recurrent and persistent hematuria with C3 glomerulopathy (N02.A)
N02.6Recurrent and persistent hematuria with dense deposit disease
› Recurrent and persistent hematuria with C3 glomerulopathy with dense deposit disease
› Recurrent and persistent hematuria with membranoproliferative glomerulonephritis, type 2
N02.7Recurrent and persistent hematuria with diffuse crescentic glomerulonephritis
› Recurrent and persistent hematuria with extracapillary glomerulonephritis
N02.8Recurrent and persistent hematuria with other morphologic changes
› Recurrent and persistent hematuria with proliferative glomerulonephritis NOS
N02.9Recurrent and persistent hematuria with unspecified morphologic changes
N02.ARecurrent and persistent hematuria with C3 glomerulonephritis
› Recurrent and persistent hematuria with C3 glomerulopathy
Excludes 1: Recurrent and persistent hematuria (with C3 glomerulopathy) with dense deposit disease (N02.6)
N02.BRecurrent and persistent immunoglobulin A nephropathy
N02.B1Recurrent and persistent immunoglobulin A nephropathy with glomerular lesion
N02.B2Recurrent and persistent immunoglobulin A nephropathy with focal and segmental glomerular lesion
› Recurrent and persistent immunoglobulin A nephropathy with focal and segmental hyalinosis or sclerosis
N02.B3Recurrent and persistent immunoglobulin A nephropathy with diffuse membranoproliferative glomerulonephritis
N02.B4Recurrent and persistent immunoglobulin A nephropathy with diffuse membranous glomerulonephritis
N02.B5Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangial proliferative glomerulonephritis
N02.B6Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangiocapillary glomerulonephritis
N02.B9Other recurrent and persistent immunoglobulin A nephropathy
N03Chronic nephritic syndrome
Includes: chronic glomerular disease
› chronic glomerulonephritis
› chronic nephritis
Excludes 1: chronic tubulo-interstitial nephritis (N11.-)
› diffuse sclerosing glomerulonephritis (N05.8-)
› nephritic syndrome NOS (N05.-)
N03.0Chronic nephritic syndrome with minor glomerular abnormality
› Chronic nephritic syndrome with minimal change lesion
N03.1Chronic nephritic syndrome with focal and segmental glomerular lesions
› Chronic nephritic syndrome with focal and segmental hyalinosis
› Chronic nephritic syndrome with focal and segmental sclerosis
› Chronic nephritic syndrome with focal glomerulonephritis
N03.2Chronic nephritic syndrome with diffuse membranous glomerulonephritis
N03.3Chronic nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N03.4Chronic nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N03.5Chronic nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
› Chronic nephritic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
Excludes 1: Chronic nephritic syndrome with C3 glomerulonephritis (N03.A)
› Chronic nephritic syndrome with C3 glomerulopathy (N03.A)
N03.6Chronic nephritic syndrome with dense deposit disease
› Chronic nephritic syndrome with C3 glomerulopathy with dense deposit disease
› Chronic nephritic syndrome with membranoproliferative glomerulonephritis, type 2
N03.7Chronic nephritic syndrome with diffuse crescentic glomerulonephritis
› Chronic nephritic syndrome with extracapillary glomerulonephritis
N03.8Chronic nephritic syndrome with other morphologic changes
› Chronic nephritic syndrome with proliferative glomerulonephritis NOS
N03.9Chronic nephritic syndrome with unspecified morphologic changes
N03.AChronic nephritic syndrome with C3 glomerulonephritis
› Chronic nephritic syndrome with C3 glomerulopathy
Excludes 1: Chronic nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N03.6)
N04Nephrotic syndrome
Includes: congenital nephrotic syndrome
› lipoid nephrosis
N04.0Nephrotic syndrome with minor glomerular abnormality
› Nephrotic syndrome with minimal change lesion
N04.1Nephrotic syndrome with focal and segmental glomerular lesions
› Nephrotic syndrome with focal and segmental hyalinosis
› Nephrotic syndrome with focal and segmental sclerosis
› Nephrotic syndrome with focal glomerulonephritis
N04.2Nephrotic syndrome with diffuse membranous glomerulonephritis
N04.20Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
› Membranous nephropathy NOS with nephrotic syndrome
N04.21Primary membranous nephropathy with nephrotic syndrome
› Idiopathic membranous nephropathy with nephrotic syndrome
N04.22Secondary membranous nephropathy with nephrotic syndrome
Code First: , if applicable, other disease or disorder or poisoning causing membranous nephropathy
Use Additional Code: code, if applicable, for adverse effect of drug causing membranous nephropathy
N04.29Other nephrotic syndrome with diffuse membranous glomerulonephritis
N04.3Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
N04.4Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
N04.5Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
Excludes 1: Nephrotic syndrome with C3 glomerulonephritis (N04.A)
› Nephrotic syndrome with C3 glomerulopathy (N04.A)
N04.6Nephrotic syndrome with dense deposit disease
› Nephrotic syndrome with C3 glomerulopathy with dense deposit disease
› Nephrotic syndrome with membranoproliferative glomerulonephritis, type 2
N04.7Nephrotic syndrome with diffuse crescentic glomerulonephritis
› Nephrotic syndrome with extracapillary glomerulonephritis
N04.8Nephrotic syndrome with other morphologic changes
› Nephrotic syndrome with proliferative glomerulonephritis NOS
N04.9Nephrotic syndrome with unspecified morphologic changes
N04.ANephrotic syndrome with C3 glomerulonephritis
› Nephrotic syndrome with C3 glomerulopathy
Excludes 1: Nephrotic syndrome (with C3 glomerulopathy) with dense deposit disease (N04.6)
N04.BNephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)
N04.B1Nephrotic syndrome with idiopathic immune complex membranoproliferative glomerulonephritis (IC-MPGN)
N04.B2Nephrotic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
N05Unspecified nephritic syndrome
Includes: glomerular disease NOS
› glomerulonephritis NOS
› nephritis NOS
› nephropathy NOS and renal disease NOS with morphological lesion specified in .0-.8
Excludes 1: nephropathy NOS with no stated morphological lesion (N28.9)
› renal disease NOS with no stated morphological lesion (N28.9)
› tubulo-interstitial nephritis NOS (N12)
N05.0Unspecified nephritic syndrome with minor glomerular abnormality
› Unspecified nephritic syndrome with minimal change lesion
N05.1Unspecified nephritic syndrome with focal and segmental glomerular lesions
› Unspecified nephritic syndrome with focal and segmental hyalinosis
› Unspecified nephritic syndrome with focal and segmental sclerosis
› Unspecified nephritic syndrome with focal glomerulonephritis
N05.2Unspecified nephritic syndrome with diffuse membranous glomerulonephritis
N05.3Unspecified nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
N05.4Unspecified nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
N05.5Unspecified nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
› Unspecified nephritic syndrome with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
Excludes 1: Unspecified nephritic syndrome with C3 glomerulonephritis (N05.A)
› Unspecified nephritic syndrome with C3 glomerulopathy (N05.A)
N05.6Unspecified nephritic syndrome with dense deposit disease
› Unspecified nephritic syndrome with C3 glomerulopathy with dense deposit disease
› Unspecified nephritic syndrome with membranoproliferative glomerulonephritis, type 2
N05.7Unspecified nephritic syndrome with diffuse crescentic glomerulonephritis
› Unspecified nephritic syndrome with extracapillary glomerulonephritis
N05.8Unspecified nephritic syndrome with other morphologic changes
› Unspecified nephritic syndrome with proliferative glomerulonephritis NOS
N05.9Unspecified nephritic syndrome with unspecified morphologic changes
N05.AUnspecified nephritic syndrome with C3 glomerulonephritis
› Unspecified nephritic syndrome with C3 glomerulopathy
Excludes 1: Unspecified nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N05.6)
N06Isolated proteinuria with specified morphological lesion
Excludes 1: Proteinuria not associated with specific morphologic lesions (R80.0)
N06.0Isolated proteinuria with minor glomerular abnormality
› Isolated proteinuria with minimal change lesion
N06.1Isolated proteinuria with focal and segmental glomerular lesions
› Isolated proteinuria with focal and segmental hyalinosis
› Isolated proteinuria with focal and segmental sclerosis
› Isolated proteinuria with focal glomerulonephritis
N06.2Isolated proteinuria with diffuse membranous glomerulonephritis
N06.20Isolated proteinuria with diffuse membranous glomerulonephritis, unspecified
› Membranous nephropathy, NOS
Excludes 1: membranous nephropathy NOS with nephrotic syndrome (N04.20)
N06.21Primary membranous nephropathy with isolated proteinuria
› Idiopathic membranous nephropathy (with isolated proteinuria)
› Primary membranous nephropathy, NOS
Excludes 1: primary membranous nephropathy with nephrotic syndrome (N04.21)
N06.22Secondary membranous nephropathy with isolated proteinuria
› Secondary membranous nephropathy, NOS
Code First: , if applicable, other disease or disorder or poisoning causing membranous nephropathy
Use Additional Code: code, if applicable, for adverse effect of drug causing membranous nephropathy
Excludes 1: secondary membranous nephropathy with nephrotic syndrome (N04.22)
N06.29Other isolated proteinuria with diffuse membranous glomerulonephritis
N06.3Isolated proteinuria with diffuse mesangial proliferative glomerulonephritis
N06.4Isolated proteinuria with diffuse endocapillary proliferative glomerulonephritis
N06.5Isolated proteinuria with diffuse mesangiocapillary glomerulonephritis
› Isolated proteinuria with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
Excludes 1: Isolated proteinuria with C3 glomerulonephritis (N06.A)
› Isolated proteinuria with C3 glomerulopathy (N06.A)
N06.6Isolated proteinuria with dense deposit disease
› Isolated proteinuria with C3 glomerulopathy with dense deposit disease
› Isolated proteinuria with membranoproliferative glomerulonephritis, type 2
N06.7Isolated proteinuria with diffuse crescentic glomerulonephritis
› Isolated proteinuria with extracapillary glomerulonephritis
N06.8Isolated proteinuria with other morphologic lesion
› Isolated proteinuria with proliferative glomerulonephritis NOS
N06.9Isolated proteinuria with unspecified morphologic lesion
N06.AIsolated proteinuria with C3 glomerulonephritis
› Isolated proteinuria with C3 glomerulopathy
Excludes 1: Isolated proteinuria (with C3 glomerulopathy) with dense deposit disease (N06.6)
N07Hereditary nephropathy, not elsewhere classified
Excludes 2: Alport's syndrome (Q87.81-)
› hereditary amyloid nephropathy (E85.-)
› nail patella syndrome (Q87.2)
› non-neuropathic heredofamilial amyloidosis (E85.-)
N07.0Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
› Hereditary nephropathy, not elsewhere classified with minimal change lesion
N07.1Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
› Hereditary nephropathy, not elsewhere classified with focal and segmental hyalinosis
› Hereditary nephropathy, not elsewhere classified with focal and segmental sclerosis
› Hereditary nephropathy, not elsewhere classified with focal glomerulonephritis
N07.2Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
N07.3Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
N07.4Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
N07.5Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
› Hereditary nephropathy, not elsewhere classified with membranoproliferative glomerulonephritis, types 1 and 3, or NOS
Excludes 1: Hereditary nephropathy, not elsewhere classified with C3 glomerulonephritis (N07.A)
› Hereditary nephropathy, not elsewhere classified with C3 glomerulopathy (N07.A)
N07.6Hereditary nephropathy, not elsewhere classified with dense deposit disease
› Hereditary nephropathy, not elsewhere classified with C3 glomerulopathy with dense deposit disease
› Hereditary nephropathy, not elsewhere classified with membranoproliferative glomerulonephritis, type 2
N07.7Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
› Hereditary nephropathy, not elsewhere classified with extracapillary glomerulonephritis
N07.8Hereditary nephropathy, not elsewhere classified with other morphologic lesions
› Hereditary nephropathy, not elsewhere classified with proliferative glomerulonephritis NOS
N07.9Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
N07.AHereditary nephropathy, not elsewhere classified with C3 glomerulonephritis
› Hereditary nephropathy, not elsewhere classified with C3 glomerulopathy
Excludes 1: Hereditary nephropathy, not elsewhere classified (with C3 glomerulopathy) with dense deposit disease (N07.6)
N07.BHereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]
› AMKD (with glomerulonephritis)
› AMKD (with glomerulosclerosis)
N08Glomerular disorders in diseases classified elsewhere
› Glomerulonephritis
› Nephritis
› Nephropathy
Code First: underlying disease, such as:
› amyloidosis (E85.-)
› congenital syphilis (A50.5)
› cryoglobulinemia (D89.1)
› disseminated intravascular coagulation (D65)
› gout (M1A.-, M10.-)
› microscopic polyangiitis (M31.7)
› multiple myeloma (C90.0-)
› sepsis (A40.0-A41.9)
› sickle-cell disease (D57.0-D57.8)
Excludes 1: glomerulonephritis, nephritis and nephropathy (in):
› antiglomerular basement membrane disease (M31.0)
› diabetes (E08-E13 with .21)
› gonococcal (A54.21)
› Goodpasture's syndrome (M31.0)
› hemolytic-uremic syndrome (D59.3-)
› lupus (M32.14)
› mumps (B26.83)
› syphilis (A52.75)
› systemic lupus erythematosus (M32.14)
› Wegener's granulomatosis (M31.31)
› pyelonephritis in diseases classified elsewhere (N16)
› renal tubulo-interstitial disorders classified elsewhere (N16)