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List of Diseases and Injuries

Aplastic and other anemias and other bone marrow failure syndromes (D60-D64)

D60Acquired pure red cell aplasia [erythroblastopenia]
Includes: red cell aplasia (acquired) (adult) (with thymoma)

Excludes 1: congenital red cell aplasia (D61.01)

D60.0Chronic acquired pure red cell aplasia

D60.1Transient acquired pure red cell aplasia

D60.8Other acquired pure red cell aplasias

D60.9Acquired pure red cell aplasia, unspecified

D61Other aplastic anemias and other bone marrow failure syndromes
Excludes 2: neutropenia (D70.-)

D61.0Constitutional aplastic anemia

D61.01Constitutional (pure) red blood cell aplasia
Blackfan-Diamond syndrome
Congenital (pure) red cell aplasia
Familial hypoplastic anemia
Primary (pure) red cell aplasia
Red cell (pure) aplasia of infants

Excludes 1: acquired red cell aplasia (D60.9)

D61.02Shwachman-Diamond syndrome
Code Also: , if applicable, associated conditions such as:
acute myeloblastic leukemia (C92.0-)
exocrine pancreatic insufficiency (K86.81)
myelodysplastic syndrome (D46.-)

Use Additional Code: code, if applicable, for genetic susceptibility to other malignant neoplasm (Z15.09)

D61.09Other constitutional aplastic anemia
Fanconi's anemia
Pancytopenia with malformations

D61.1Drug-induced aplastic anemia
Use Additional Code: code for adverse effect, if applicable, to identify drug (T36-T50) with fifth or sixth character 5)

D61.2Aplastic anemia due to other external agents
Code First: , if applicable, toxic effects of substances chiefly nonmedicinal as to source (T51-T65)

D61.3Idiopathic aplastic anemia

D61.8Other specified aplastic anemias and other bone marrow failure syndromes

D61.81Pancytopenia
Excludes 1: pancytopenia (due to) (with) aplastic anemia (D61.9)
pancytopenia (due to) (with) bone marrow infiltration (D61.82)
pancytopenia (due to) (with) congenital (pure) red cell aplasia (D61.01)
pancytopenia (due to) (with) hairy cell leukemia (C91.4-)
pancytopenia (due to) (with) human immunodeficiency virus disease (B20.-)
pancytopenia (due to) (with) leukoerythroblastic anemia (D61.82)
pancytopenia (due to) (with) myeloproliferative disease (D47.1)

Excludes 2: pancytopenia (due to) (with) myelodysplastic syndromes (D46.-)

D61.810Antineoplastic chemotherapy induced pancytopenia
Excludes 2: aplastic anemia due to antineoplastic chemotherapy (D61.1)

D61.811Other drug-induced pancytopenia
Excludes 2: aplastic anemia due to drugs (D61.1)

D61.818Other pancytopenia

D61.82Myelophthisis
Leukoerythroblastic anemia
Myelophthisic anemia
Panmyelophthisis

Code Also: the underlying disorder, such as:
malignant neoplasm of breast (C50.-)
tuberculosis (A15.-)

Excludes 1: idiopathic myelofibrosis (D47.1)
myelofibrosis NOS (D75.81)
myelofibrosis with myeloid metaplasia (D47.4)
primary myelofibrosis (D47.1)
secondary myelofibrosis (D75.81)

D61.89Other specified aplastic anemias and other bone marrow failure syndromes

D61.9Aplastic anemia, unspecified
Hypoplastic anemia NOS
Medullary hypoplasia

D62Acute posthemorrhagic anemia
Excludes 1: anemia due to chronic blood loss (D50.0)
blood loss anemia NOS (D50.0)
congenital anemia from fetal blood loss (P61.3)

D63Anemia in chronic diseases classified elsewhere

D63.0Anemia in neoplastic disease
Code First: neoplasm (C00-D49)

Excludes 1: aplastic anemia due to antineoplastic chemotherapy (D61.1)

Excludes 2: anemia due to antineoplastic chemotherapy (D64.81)

D63.1Anemia in chronic kidney disease
Erythropoietin resistant anemia (EPO resistant anemia)

Code First: underlying chronic kidney disease (CKD) (N18.-)

D63.8Anemia in other chronic diseases classified elsewhere
Code First: underlying disease, such as:
diphyllobothriasis (B70.0)
hookworm disease (B76.0-B76.9)
hypothyroidism (E00.0-E03.9)
malaria (B50.0-B54)
symptomatic late syphilis (A52.79)
tuberculosis (A18.89)

D64Other anemias
Excludes 1: refractory anemia (D46.-)
refractory anemia with excess blasts in transformation [RAEB T] (C92.0-)

D64.0Hereditary sideroblastic anemia
Sex-linked hypochromic sideroblastic anemia

D64.1Secondary sideroblastic anemia due to disease
Code First: underlying disease

D64.2Secondary sideroblastic anemia due to drugs and toxins
Code First: poisoning due to drug or toxin, if applicable (T36-T65 with fifth or sixth character 1-4)

Use Additional Code: code for adverse effect, if applicable, to identify drug (T36-T50) with fifth or sixth character 5)

D64.3Other sideroblastic anemias
Sideroblastic anemia NOS
Pyridoxine-responsive sideroblastic anemia NEC

D64.4Congenital dyserythropoietic anemia
Dyshematopoietic anemia (congenital)

Excludes 1: Blackfan-Diamond syndrome (D61.01)
Di Guglielmo's disease (C94.0)

D64.8Other specified anemias

D64.81Anemia due to antineoplastic chemotherapy
Antineoplastic chemotherapy induced anemia

Excludes 2: anemia in neoplastic disease (D63.0)
aplastic anemia due to antineoplastic chemotherapy (D61.1)

D64.89Other specified anemias
Infantile pseudoleukemia

D64.9Anemia, unspecified