Rare but increasingly described primary immunodeficiencies that cause homeostatic dysregulation of the immune system either alone or in association with increased vulnerability to infection (Table 157-1).
For a more detailed discussion, see Fischer A: Primary Immune Deficiency Diseases, Chap. 374, p. 2103, in HPIM-19. |
Section 12. Allergy, Clinical Immunology, and Rheumatology